{"orpha":263310,"name":"Thymoma type A","type":"Histopathological subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This disease is described under Thymoma","url":"https://raremap.alftech.space/d/ORPHA-263310/","orphanet_url":"https://www.orpha.net/en/disease/detail/263310","names":{"fr":{"name":"Thymome type A"},"de":{"name":"Thymom Typ A"},"es":{"name":"Timoma tipo A"},"it":{"name":"Timoma, tipo A","synonyms":["Neoplasia epiteliale primitiva del timo, tipo A","Tumore epiteliale primitivo del timo, tipo A"]},"nl":{"name":"Thymoom type A"},"pt":{"name":"Timoma tipo A"},"pl":{"name":"Grasiczak typu A","synonyms":["Pierwotny guz nabłonkowy grasicy typu A","Pierwotny nowotwór nabłonkowy grasicy typu A"]},"cs":{"name":"Thymom, typ A","synonyms":["Primární epiteliální neoplázie thymu, typ A","Primární epiteliální nádor thymu, typ A"]},"uk":{"name":"Тимома, тип А","synonyms":["Первинне епітеліальне новоутворення тимуса, тип А","Первинна епітеліальна пухлина тимуса, тип А"]},"zh":{"name":"A型胸腺瘤","synonyms":["A型原发性胸腺上皮性肿瘤"]},"tr":{"name":"Timoma tip A","synonyms":["Primer timik epitelyal tümörü tipA","Primer timik epitelyal neoplazma tipA"]}},"xrefs":[{"source":"ICD-10","code":"C37","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"D15.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2C27.2","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1120130061"},{"source":"ICD-11","code":"XH6WN9","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1258154589"},{"source":"MONDO","code":"0002588","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1266091","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":99867,"name":"Thymoma","classifications":[202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Annual incidence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe 2011[OTHER]"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}