{"orpha":254449,"name":"Atrophic lichen planus","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Atrophic LP"],"definition":"A rare variant of cutaneous lichen planus characterized by the development of pale papules or plaques with an atrophic center.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-254449/","orphanet_url":"https://www.orpha.net/en/disease/detail/254449","names":{"fr":{"name":"Lichen plan atrophique","synonyms":["LP atrophique"],"definition":"Le lichen plan (LP) atrophique est une variante rare de LP cutané caractérisée par l'éruption de papules ou de plaques pâles à centre atrophique."},"de":{"name":"Lichen planus atrophicans","synonyms":["LP, atrophischer"],"definition":"Der Atrophische Lichen planus (LP) ist eine seltene Variante des kutanen Lichen planus und gekennzeichnet durch das Auftreten blasser Papeln oder Plaques mit atrophischem Zentrum."},"es":{"name":"Liquen plano atrófico","definition":"Es una variante poco frecuente del liquen plano cutáneo caracterizado por el desarrollo de pápulas pálidas o placas con atrofia central."},"it":{"name":"Lichen planus atrofico","synonyms":["LP atrofico"],"definition":"Il lichen piano (LP) atrofico è una variante rara del lichen piano cutaneo (si veda questo termine), caratterizzata dallo sviluppo di papule o placche chiare con una parte centrale atrofica."},"nl":{"name":"Atrofische lichen planus","synonyms":["Atrofische LP"],"definition":"Een zeldzame variant van cutane lichen planus, gekarakteriseerd door de ontwikkeling van bleke papels of plaques met een atrofisch centrum."},"pt":{"name":"Líquen plano atrófico","synonyms":["LP atrófico"],"definition":"O líquen plano (LP) atrófico é uma variante rara de líquen plano cutâneo (ver este termo) caracterizado pelo desenvolvimento de pápulas ou placas pálidas com um centro atrófico."},"pl":{"name":"Liszaj płaski zanikowy","synonyms":["LP zanikowy"]},"cs":{"name":"Atrofický lichen planus","synonyms":["Atrofický LP"]},"uk":{"name":"Атрофічний червоний плескатий лишай","synonyms":["Атрофічна LP"],"definition":"A rare variant of cutaneous lichen planus characterized by the development of pale papules or plaques with an atrophic center."},"zh":{"name":"萎缩性扁平苔藓","synonyms":["萎缩性LP"],"definition":"一种罕见的皮肤扁平苔藓变种，其特征是形成苍白的丘疹或带有萎缩中心的斑块。"},"tr":{"name":"Atrofik liken planus","synonyms":["Atrofik LP"]}},"xrefs":[{"source":"ICD-10","code":"L43.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EA91.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1633911307"},{"source":"MONDO","code":"0016773","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0023647","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12675","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10056959","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":254370,"name":"Rare cutaneous lichen planus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}