{"orpha":254424,"name":"Annular lichen planus","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Annular LP"],"definition":"A rare variant of cutaneous lichen planus characterized by the development of annular lesions.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-254424/","orphanet_url":"https://www.orpha.net/en/disease/detail/254424","names":{"fr":{"name":"Lichen plan annulaire","synonyms":["LP annulaire"],"definition":"Le lichen plan (LP) annulaire est une variante rare de LP cutané caractérisée par l'éruption de lésions annulaires."},"de":{"name":"Lichen planus anularis","synonyms":["LP, anulärer"],"definition":"Der Annuläre Lichen planus (LP) ist eine seltene Variante des kutanen Lichen planus (s. dort) und gekennzeichnet durch das Auftreten annulärer Läsionen."},"es":{"name":"Liquen plano anular","definition":"Es una variante rara del liquen plano (LP) cutáneo caracterizado por el desarrollo de lesiones anulares."},"it":{"name":"Lichen planus anulare","synonyms":["LP anulare"],"definition":"Il lichen piano (LP) anulare è una variante rara del lichen piano cutaneo (si veda questo termine), caratterizzata dallo sviluppo di lesioni anulari."},"nl":{"name":"Annulaire lichen planus","synonyms":["Annulaire LP","Ringvormige lichen planus"],"definition":"Een zeldzame, cutane lichen planus, gekarakteriseerd door ontwikkeling van ringvormige laesies."},"pt":{"name":"Líquen plano anular","synonyms":["LP anular"],"definition":"O líquen plano (LP) anular é uma variante rara de líquen plano cutâneo (ver este termo), caracterizado pelo desenvolvimento de lesões anulares."},"pl":{"name":"Liszaj płaski pierścieniowy","synonyms":["LP pierścieniowy"]},"cs":{"name":"Anulární lichen planus","synonyms":["Anulární LP"]},"uk":{"name":"Кільцеподібний плескатий лишай","synonyms":["Кільцева LP"],"definition":"A rare variant of cutaneous lichen planus characterized by the development of annular lesions."},"zh":{"name":"环状扁平苔藓","synonyms":["环状LP"],"definition":"一种罕见的皮肤扁平苔藓变种，以环状病变发展为特征。"},"tr":{"name":"Halka şeklindeki liken planus","synonyms":["Annular LP"]}},"xrefs":[{"source":"ICD-10","code":"L43.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EA91.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"206328727"},{"source":"MONDO","code":"0016772","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0406363","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12674","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":254370,"name":"Rare cutaneous lichen planus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}