{"orpha":252057,"name":"Tumor of cranial and spinal nerves","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["Rare tumor of cranial and spinal nerves"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-252057/","orphanet_url":"https://www.orpha.net/en/disease/detail/252057","names":{"fr":{"name":"Tumeur des nerfs crâniens et spinaux","synonyms":["Tumeur rare des nerfs crâniens et rachidiens","Tumeur rare des nerfs crâniens et spinaux"]},"de":{"name":"Tumoren der kranialen und spinalen Nerven","synonyms":["Seltene Tumoren der kranialen und spinalen Nerven"]},"es":{"name":"Tumor de los nervios craneales y espinales","synonyms":["Tumor raro de los nervios craneales y espinales"]},"it":{"name":"Tumore dei nervi cranici e spinali","synonyms":["Tumore raro dei nervi cranici e spinali"]},"nl":{"name":"Tumor van craniale en spinale zenuwen","synonyms":["Zeldzame tumor van craniale en spinale zenuwen"]},"pt":{"name":"Tumor dos nervos cranianos e espinhais"},"pl":{"name":"Guz nerwów czaszkowych i rdzeniowych","synonyms":["Rzadki guz nerwów czaszkowych i rdzeniowych"]},"cs":{"name":"Nádor kraniálních a spinálních nervů","synonyms":["Vzácný nádor kraniálních a spinálních nervů"]},"uk":{"name":"Пухлина черепно-мозкових і спинномозкових нервів","synonyms":["Рідкісна пухлина черепно-мозкових та спинномозкових нервів"]},"zh":{"name":"颅、脊神经瘤","synonyms":["颅神经和脊神经罕见性肿瘤"]},"tr":{"name":"Kraniyal ve spinal sinirlerin tümörü","synonyms":["Nadir kraniyal ve spinal sinir tümörü"]}},"xrefs":[{"source":"MONDO","code":"0016749","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"16749","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679636","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12697","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":98062,"name":"Rare nervous system tumor","classifications":[181,202]}],"children":[{"orpha":252131,"name":"Benign peripheral nerve sheath tumor","type":"Category"},{"orpha":3148,"name":"Malignant peripheral nerve sheath tumor","type":"Disease"},{"orpha":2086,"name":"Optic pathway glioma","type":"Disease"},{"orpha":85102,"name":"Perineurioma","type":"Clinical group"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":1.89,"area":"United States","status":"Validated","source":"Central Brain Tumor OTHERistry of the United States 2010-2014[OTHER]_29117289[PMID]"}],"phenotypes":null}