{"orpha":251896,"name":"Choroid plexus tumor","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-251896/","orphanet_url":"https://www.orpha.net/en/disease/detail/251896","names":{"fr":{"name":"Tumeur des plexus choroïdes"},"de":{"name":"Choroidplexustumor"},"es":{"name":"Tumor del plexo coroideo"},"it":{"name":"Tumore del plesso corioideo"},"nl":{"name":"Tumor van plexus choroideus","synonyms":["Plexus choroideus-tumor"]},"pt":{"name":"Tumor do plexo coróide"},"pl":{"name":"Guz splotu naczyniówkowego"},"cs":{"name":"Nádor choroidálního plexu"},"uk":{"name":"Пухлина судинного сплетення"},"zh":{"name":"脉络丛瘤"},"tr":{"name":"Koroid pleksus tümörü"}},"xrefs":[{"source":"ICD-11","code":"2A00.22","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1959912502"},{"source":"MONDO","code":"0016717","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"16717","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D016545","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0085138","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":251558,"name":"Rare tumor of neuroepithelial tissue","classifications":[181,202]}],"children":[{"orpha":251902,"name":"Atypical papilloma of choroid plexus","type":"Disease"},{"orpha":251899,"name":"Choroid plexus carcinoma","type":"Disease"},{"orpha":2807,"name":"Papilloma of choroid plexus","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.05,"area":"United States","status":"Validated","source":"Central Brain Tumor OTHERistry of the United States 2010-2014[OTHER]_29117289[PMID]"}],"phenotypes":null}