{"orpha":231637,"name":"Rare surgically correctable form of primary aldosteronism","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":"A rare primary hyperaldosteronism characterized by unilateral aldosterone hypersecretion and renin suppression, associated with varying degrees of hypertension and hypokalemia.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-231637/","orphanet_url":"https://www.orpha.net/en/disease/detail/231637","names":{"fr":{"name":"Hyperaldostéronisme primitif rare traitable chirurgicalement"},"de":{"name":"Seltene chirurgisch korrigierbar Formen des primären Hyperaldosteronismus"},"es":{"name":"Hiperaldosteronismo primario raro corregible por cirugía","definition":"Las formas de aldosteronismo primario corregibles quirúrgicamente (también conocidas como hiperaldosteronismo primario) se caracterizan por hipersecreción unilateral de aldosterona y supresión de renina, asociadas con diversos grados de hipertensión e hipopotasemia."},"it":{"name":"Iperaldosteronismo primitivo raro corregibile chirurgicamente"},"nl":{"name":"Zeldzame chirurgisch corrigeerbare vorm van primair aldosteronisme","definition":"Chirurgisch corrigeerbare vormen van primair aldosteronisme (ook gekend als primair hyperaldosteronisme) worden gekenmerkt door unilaterale hypersecretie van aldosteron en suppressie van renine, geassocieerd met variabele gradaties van hypertensie en hypokaliëmie."},"pt":{"name":"Hiperaldosteronismo primário raro corrigível cirurgicamente"},"pl":{"name":"Rzadka forma pierwotnego aldosteronizmu możliwa do korekcji chirurgicznej"},"cs":{"name":"Vzácná chirurgicky odstranitelná forma primárního aldosteronismu"},"uk":{"name":"Рідкісна форма первинного альдостеронізму, що піддається хірургічній корекції","definition":"A rare primary hyperaldosteronism characterized by unilateral aldosterone hypersecretion and renin suppression, associated with varying degrees of hypertension and hypokalemia."},"zh":{"name":"罕见手术可纠正型原发性醛固酮症","definition":"外科手术纠正的原发性醛固酮症（也称原发性醛固酮增多症；见该词条）的特点是单侧醛固酮分泌增多和肾素分泌抑制，伴有不同程度的高血压和低钾血症。"},"tr":{"name":"Primer aldosteronizmin nadir cerrahi olarak düzeltilebilir formu"}},"xrefs":[{"source":"MONDO","code":"16507","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680925","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97978,"name":"Rare endocrine disease"},"parents":[{"orpha":181415,"name":"Rare primary hyperaldosteronism","classifications":[193]}],"children":[{"orpha":231625,"name":"Adrenocortical carcinoma with pure aldosterone hypersecretion","type":"Disease"},{"orpha":369929,"name":"Primary hyperaldosteronism-seizures-neurological abnormalities syndrome","type":"Disease"},{"orpha":231580,"name":"Primary unilateral adrenal hyperplasia","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}