{"orpha":217071,"name":"Renal cell carcinoma","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["RCC"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-217071/","orphanet_url":"https://www.orpha.net/en/disease/detail/217071","names":{"fr":{"name":"Carcinome rénal","synonyms":["RCC"]},"de":{"name":"Nierenzellkarzinom","synonyms":["RCC"]},"es":{"name":"Carcinoma de células renales","synonyms":["CCR"]},"it":{"name":"Carcinoma delle cellule renali","synonyms":["RCC"]},"nl":{"name":"Niercelcarcinoom","synonyms":["RCC","Renaalcelcarcinoom"]},"pt":{"name":"Carcinoma de células renais"},"pl":{"name":"Rak nerkowokomórkowy","synonyms":["RCC"]},"cs":{"name":"Karcinom ledviny","synonyms":["RCC"]},"uk":{"name":"Нирково-клітинна карцинома","synonyms":["RCC"]},"zh":{"name":"肾细胞癌","synonyms":["RCC"]},"tr":{"name":"Renal hücreli karsinom","synonyms":["SSB"]}},"xrefs":[{"source":"ICD-11","code":"2C90.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"825917541"},{"source":"MONDO","code":"0005086","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"5086","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D002292","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0007134","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"13215","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10067946","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[{"type":"Referred to","orpha":319314,"name":"OBSOLETE: Renal cell carcinoma associated with neuroblastoma","status":"inactive"}],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":506213,"name":"Rare disorder potentially indicated for kidney transplant","classifications":[233]},{"orpha":93619,"name":"Rare renal tumor","classifications":[188,202]}],"children":[{"orpha":404514,"name":"Acquired cystic disease-associated renal cell carcinoma","type":"Disease"},{"orpha":319303,"name":"Chromophobe renal cell carcinoma","type":"Disease"},{"orpha":319276,"name":"Clear cell renal carcinoma","type":"Disease"},{"orpha":247203,"name":"Collecting duct carcinoma","type":"Disease"},{"orpha":319308,"name":"MiT family translocation renal cell carcinoma","type":"Disease"},{"orpha":319322,"name":"Mucinous tubular and spindle cell renal carcinoma","type":"Disease"},{"orpha":319298,"name":"Papillary renal cell carcinoma","type":"Disease"},{"orpha":319319,"name":"Renal medullary carcinoma","type":"Disease"},{"orpha":319325,"name":"Tubulocystic renal cell carcinoma","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Value and class","class":"1-5 / 10 000","value":42.0,"area":"Europe","status":"Validated","source":"European Medicines Agency 2010[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":8.35,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"}],"phenotypes":null}