{"orpha":209973,"name":"Benign nocturnal alternating hemiplegia of childhood","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Benign nocturnal alternating hemiplegia of childhood is a rare neurologic disease characterized by recurrent attacks of nocturnal screaming or crying followed or accompanied by unilateral or sometimes bilateral hemiplegia. Disorder is not associated with neurological or developmental impairments but may be associated with mild behavioral abnormalities.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-209973/","orphanet_url":"https://www.orpha.net/en/disease/detail/209973","names":{"fr":{"name":"Hémiplégie alternante nocturne bénigne de l'enfance","definition":"Une maladie neurologique rare caractérisée par des crises nocturnes récurrentes de hurlements ou de pleurs, suivis ou accompagnés par une hémiplégie unilatérale ou parfois bilatérale. Il n'y a pas d'atteinte neurologique ou du développement associée, mais la maladie peut être associée à de légers troubles du comportement."},"de":{"name":"Benigne nächtliche alternierende Hemiplegie im Kindesalter","synonyms":["BNAHC"],"definition":"Die benigne nächtliche alternierende Hemiplegie des Kindesalters ist eine seltene neurologische Erkrankung, die durch wiederkehrende nächtliche Schreianfälle gekennzeichnet ist, die von einer einseitigen oder manchmal auch beidseitigen Hemiplegie begleitet werden. Die Störung geht nicht mit neurologischen oder entwicklungsbedingten Beeinträchtigungen einher, kann aber mit leichten Verhaltensauffälligkeiten verbunden sein."},"es":{"name":"Hemiplejía alternante nocturna benigna de la infancia","definition":"Es una enfermedad neurológica poco frecuente caracterizada por ataques recurrentes de gritos o llantos nocturnos seguidos o acompañados por hemiplejia unilateral o, en ocasiones, bilateral. El trastorno no se asocia a alteraciones neurológicas o del desarrollo pero puede asociarse a leves trastornos de conducta."},"it":{"name":"Emiplegia alternante notturna benigna del bambino","synonyms":["Emiplegia alternante familiare notturna benigna dell'infanzia"],"definition":"L'emiplegia alternante notturna benigna del bambino è una malattia neurologica rara, caratterizzata da episodi ricorrenti di urla o pianti notturni seguiti o accompagnati da emiplegia monolaterale o, occasionalmente, bilaterale. La malattia non si associa a deficit neurologici o dello sviluppo, ma può associarsi a lievi anomalie comportamentali."},"nl":{"name":"Benigne nachtelijke alternerende hemiplegie op kinderleeftijd","synonyms":["Goedaardige familiale nachtelijke alternerende hemiplegie in de kindertijd"],"definition":"Goedaardige nachtelijke alternerende hemiplegie in de kindertijd is een zeldzame neurologische ziekte die gekarakteriseerd wordt door recurrente aanvallen van nachtelijk schreeuwen of wenen gevolgd door of gepaard met unilaterale of soms bilaterale hemiplegie. De aandoening is niet geassocieerd met neurologische of ontwikkelingsstoornissen, maar kan geassocieerd zijn met milde gedragsafwijkingen."},"pt":{"name":"Hemiplegia alternante noturna benigna da infância"},"pl":{"name":"Łagodne nocne naprzemienne dziecięce porażenie połowicze","synonyms":["Łagodna nocna naprzemienna hemiplegia dziecięca"],"definition":"*Łagodne nocne naprzemienne dziecięce porażenie połowicze jest rzadką chorobą neurologiczną, która charakteryzuje się nawracającymi atakami nocnego krzyku lub płaczu, po których następuje lub jednoczasowo towarzyszy jednostronne lub czasami obustronne porażenie połowicze. Schorzenie to nie jest zaburza funkcji okładu nerwowego i nie wpływa negatywnie na rozwój, ale może być związane z łagodnymi zaburzeniami zachowania."},"cs":{"name":"Benigní infantilní familiární noční alternující hemiplegie","synonyms":["BNAHC","Benigní familiární noční alternující hemiplegie v dětství"]},"uk":{"name":"Доброякісна нічна альтернуюча геміплегія дитячого віку","definition":"Benign nocturnal alternating hemiplegia of childhood is a rare neurologic disease characterized by recurrent attacks of nocturnal screaming or crying followed or accompanied by unilateral or sometimes bilateral hemiplegia. Disorder is not associated with neurological or developmental impairments but may be associated with mild behavioral abnormalities."},"zh":{"name":"儿童良性夜间交替性偏瘫","definition":"儿童良性夜间交替性偏瘫是一种罕见的神经系统疾病，其主要临床表现为夜间反复出现尖叫或哭闹，同时或之后出现单侧或双侧偏瘫。该病与精神障碍或发育障碍无关，但可能与轻度行为异常有关。"},"tr":{"name":"Çocukluğun selim gece değişen hemiplejisi"}},"xrefs":[{"source":"ICD-10","code":"G81.9","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0016209","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4749822","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":209978,"name":"Alternating hemiplegia","classifications":[156,181]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Unknown"],"onset":["Childhood","Infancy"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":12.0,"area":"Worldwide","status":"Validated","source":"23820111[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET_23820111[PMID]"}],"phenotypes":null}