{"orpha":206470,"name":"Cystadenoma of childhood","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Cystadenoma of ovary in childhood"],"definition":"A benign epithelial ovarian tumor characterized by a usually unilateral, cystic, unilocular or multilocular lesion with a thin wall or septa and no intracystic solid portion on imaging. It often presents with abdominal pain or an asymptomatic abdominal mass and can be associated with ovarian torsion or malignant transformation.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-206470/","orphanet_url":"https://www.orpha.net/en/disease/detail/206470","names":{"fr":{"name":"Cystoadénome de l'enfant","synonyms":["Cystadénome ovarien de l'enfant"],"definition":"Tumeur épithéliale bénigne de l'ovaire caractérisée par une lésion unilatérale, kystique, uniloculaire ou multiloculaire avec une paroi mince ou des septa, en l'absence d'une partie solide intrakystique à l'imagerie. Elle se manifeste souvent par des douleurs abdominales ou une masse abdominale asymptomatique et peut être associée à une torsion d'annexe ou à une transformation maligne."},"de":{"name":"Zystadenom im Kindesalter","synonyms":["Zystadenom des Ovars im Kindesalter"],"definition":"Ein gutartiger epithelialer Ovarialtumor, der durch eine in der Regel unilaterale, zystische, unilokuläre oder multilokuläre Läsion mit dünner Wand oder Septen und ohne intrazystischen festen Anteil in der Bildgebung gekennzeichnet ist. Er präsentiert sich oft mit abdominalen Schmerzen oder einer asymptomatischen abdominalen Masse und kann mit einer Ovarialtorsion oder einer malignen Transformation assoziiert sein."},"es":{"name":"Cistoadenoma de la infancia","synonyms":["Cistoadenoma de ovario en la infancia"],"definition":"Es un tumor epitelial ovárico benigno caracterizado por una lesión generalmente unilateral, quística, uni- o multilocular con una pared delgada o septos y sin porción sólida intraquística en los estudios de imagen. A menudo, se presenta con dolor abdominal o con una masa abdominal asintomática y puede asociarse a torsión ovárica o transformación maligna."},"it":{"name":"Cistadenoma mucinoso o sieroso dell'infanzia","definition":"Il cistadenoma mucinoso o sieroso dell'infanzia è un tumore benigno dell'epitelio ovarico, caratterizzato da una lesione di solito monolaterale, cistica, uniloculare o multiloculare, con pareti o setti sottili, in assenza di una porzione solida intracistica sulle immagini diagnostiche. Spesso esordisce con dolore addominale o con una massa addominale indolore; può associarsi a torsione ovarica o ad una evoluzione maligna."},"nl":{"name":"Cystadenoom in de kindertijd","synonyms":["Cystadenoom van ovarium in de kindertijd"],"definition":"Een goedaardige epitheliale tumor van ovarium, gekenmerkt door een meestal unilaterale, cystische, uniloculaire of multiloculaire laesie met dunne wand of septa en geen intracystisch solide gedeelte bij beeldvorming. Het manifesteert zich vaak met abdominale pijn of een asymptomatische abdominale massa, en kan geassocieerd zijn met ovariumtorsie of maligne transformatie."},"pt":{"name":"Cistadenoma seroso ou mucinoso"},"pl":{"name":"Gruczolakotorbielak surowiczy lub śluzowy dziecięcy","synonyms":["Cystadenoma of ovary in childhood"]},"cs":{"name":"Serózní nebo mucinózní cystadenom v dětství","synonyms":["Cystadenoma of ovary in childhood"]},"uk":{"name":"Цистаденома дитячого віку","synonyms":["Цистаденома яєчника в дитячому віці"],"definition":"A benign epithelial ovarian tumor characterized by a usually unilateral, cystic, unilocular or multilocular lesion with a thin wall or septa and no intracystic solid portion on imaging. It often presents with abdominal pain or an asymptomatic abdominal mass and can be associated with ovarian torsion or malignant transformation."},"zh":{"name":"儿童囊腺病","synonyms":["儿童卵巢囊腺瘤"],"definition":"儿童浆液性或黏液性囊腺瘤是一种良性卵巢上皮性肿瘤，其特征为单侧、单房或多房的囊性病变，有薄壁或间隔，影像学表现为肿瘤内无实性结构。通常表现为腹部肿块伴或不伴腹痛，可出现卵巢扭转或肿瘤恶化。"},"tr":{"name":"Çocukluk çağı kistadenomu","synonyms":["Çocukluk çağı yumurtalık kistadenomu"]}},"xrefs":[{"source":"ICD-10","code":"D27","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2F32.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"UMLS","code":"C5679785","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":97293,"name":"Rare benign ovarian tumor","classifications":[202,205]}],"children":[{"orpha":563671,"name":"Mucinous cystadenoma of childhood","type":"Histopathological subtype"},{"orpha":563676,"name":"Seromucinous cystadenoma of childhood","type":"Histopathological subtype"},{"orpha":563666,"name":"Serous cystadenoma of childhood","type":"Histopathological subtype"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Childhood"],"prevalence":[],"phenotypes":null}