{"orpha":183672,"name":"OBSOLETE: Common variable immunodeficiency due to TNFR deficiency","type":"Etiological subtype","group":"Subtype of disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":["OBSOLETE: CVID due to TNFR deficiency"],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Common variable immunodeficiency and related disorders","url":"https://raremap.alftech.space/d/ORPHA-183672/","orphanet_url":"https://www.orpha.net/en/disease/detail/183672","names":{"fr":{"name":"OBSOLETE : Déficit immunitaire commun variable dé au déficit en TNFR","synonyms":["OBSOLETE : CVID par déficit en TNFR"]},"de":{"name":"OBSOLET: Immundefekt, kombinierter schwerer, durch TNFR-Mangel","synonyms":["OBSOLET: CVID durch TNFR-Mangel"]},"es":{"name":"OBSOLETO: Inmunodeficiencia común variable por deficiencia de TNFR","synonyms":["OBSOLETO: IDCV por deficiencia de TNFR"]},"it":{"name":"OBSOLETO: Immunodeficienza variabile comune da deficit di TNFR","synonyms":["OBSOLETO: CVID da deficit di TNFR"]},"nl":{"name":"OBSOLEET: Algemene variabele immuundeficiëntie door TNFR-deficiëntie","synonyms":["OBSOLEET: CVID door TNFR-deficiëntie"]},"pt":{"name":"OBSOLETO: Hipogamaglobulinemia por deficiência de CD19 ou ICOS"},"pl":{"name":"NIEAKTUALNE: Pospolity zmienny Niedobór odpornosci z powodu deficytu TNFR","synonyms":["NIEAKTUALNE: CVID z powodu niedoboru TNFR"]},"cs":{"name":"NEAKTUÁLNÍ: Běžná variabilní imunodeficience způsobená deficitem TNFR","synonyms":["OBSOLETE: CVID due to TNFR deficiency"]},"uk":{"name":"ЗАСТАРІЛО: Поширений варіабельний імунодефіцит внаслідок дефіциту TNFR","synonyms":["ЗАСТАРІЛО: CVID через дефіцит TNFR"]},"zh":{"name":"弃用：常见的肿瘤坏死因子受体缺陷所致多种免疫缺陷","synonyms":["TNFR基因缺陷所致CIND"]},"tr":{"name":"Eski adı: TNFR eksikliğine bağlı yaygın değişken immün yetmezlik","synonyms":["TNFR eksikliğine bağlı CVID"]}},"xrefs":[],"associations":[{"type":"Referred to","orpha":696851,"name":"Common variable immunodeficiency and related disorders"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}