{"orpha":180071,"name":"Unilateral aplasia of the Müllerian ducts","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["Unicornuate uterus"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-180071/","orphanet_url":"https://www.orpha.net/en/disease/detail/180071","names":{"fr":{"name":"Aplasie unilatérale des canaux de Müller","synonyms":["Utérus unicorne"]},"de":{"name":"Aplasie des Müller-Ganges, unilaterale","synonyms":["Uterus unicornis"]},"es":{"name":"Aplasia unilateral del conducto de Müller","synonyms":["Útero unicorne"]},"it":{"name":"Aplasia monolaterale del dotto Mülleriano","synonyms":["Utero unicorne"]},"nl":{"name":"Unilaterale aplasie van gang van Müller","synonyms":["Eenhoornige baarmoeder","Uterus unicornis"]},"pt":{"name":"Aplasia unilateral do ducto mulleriano"},"pl":{"name":"Jednostronna aplazja przewodu Müllera","synonyms":["Macica jednorożna"]},"cs":{"name":"Jednostranná aplázie Müllerových vývodů","synonyms":["Unicornuate uterus"]},"uk":{"name":"Одностороння аплазія мюллерових проток","synonyms":["Однорога матка"]},"zh":{"name":"单侧苗勒管发育不全","synonyms":["单角子宫"]},"tr":{"name":"Müllerian kanallarının unilateral aplazisi","synonyms":["Unikollis uterus"]}},"xrefs":[{"source":"ICD-10","code":"Q51.4","qualifier":"E","icd_relation":"specific","validated":true},{"source":"MONDO","code":"0015831","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"15831","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93890,"name":"Rare developmental defect during embryogenesis"},"parents":[{"orpha":73217,"name":"Müllerian aplasia","classifications":[147,156,185,205,233]}],"children":[{"orpha":180079,"name":"Pseudounicornuate uterus","type":"Morphological anomaly"},{"orpha":180074,"name":"True unicornuate uterus","type":"Morphological anomaly"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}