{"orpha":171901,"name":"Primary cutaneous T-cell lymphoma","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-171901/","orphanet_url":"https://www.orpha.net/en/disease/detail/171901","names":{"fr":{"name":"Lymphome T cutané primitif"},"de":{"name":"Primär kutanes T-Zell-Lymphom"},"es":{"name":"Linfoma cutáneo primario de células T"},"it":{"name":"Linfoma cutaneo primitivo a cellule T"},"nl":{"name":"Primair cutaan T-cellymfoom"},"pt":{"name":"Linfoma cutâneo de células T"},"pl":{"name":"Pierwotny chłoniak skóry T-komórkowy"},"cs":{"name":"Primární kožní T-buněčný lymfom"},"uk":{"name":"Первинна шкірна Т-клітинна лімфома"},"zh":{"name":"原发性皮肤T细胞淋巴瘤"},"tr":{"name":"Primer kutanöz T hücreli lenfoma"}},"xrefs":[{"source":"MONDO","code":"0015758","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"15758","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D016410","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0079773","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"6226","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10011677","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":542,"name":"Primary cutaneous lymphoma","classifications":[187,194,202,233]},{"orpha":171918,"name":"T-cell non-Hodgkin lymphoma","classifications":[194,202,233]}],"children":[{"orpha":178551,"name":"Aggressive primary cutaneous T-cell lymphoma","type":"Clinical group"},{"orpha":178548,"name":"Indolent primary cutaneous T-cell lymphoma","type":"Clinical group"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":5.2,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]_21493798[PMID]"},{"type":"Point prevalence","qualification":"Value and class","class":"1-5 / 10 000","value":24.0,"area":"Europe","status":"Validated","source":"European Medicines Agency 2012[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.09,"area":"Croatia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.097,"area":"Latvia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and 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surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.231,"area":"Switzerland","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.441,"area":"Netherlands","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.197,"area":"United Kingdom","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":1.163,"area":"Italy","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":1.57,"area":"Malta","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"}],"phenotypes":null}