{"orpha":1685,"name":"Distomatosis","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["Distomiasis","Fluke infection"],"definition":"A group of rare parasitic diseases characterized by infection with flukes with oral and ventral suckers, comprising Clonorchiasis (infection with liver flukes), Fasciolopsiasis (infection with intestinal flukes), and Paragonimiasis (infection with lung flukes). Signs and symptoms depend on the affected organ and are of variable severity. Some patients may be asymptomatic.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-1685/","orphanet_url":"https://www.orpha.net/en/disease/detail/1685","names":{"fr":{"name":"Distomatose","synonyms":["Distomiase","Infection par douve"],"definition":"Groupe de parasitoses rares caractérisées par une infection par des douves à ventouses orales et ventrales, comprenant la clonorchiase (infection par des douves hépatiques), la fasciolopsiose (infection par des douves intestinales) et la paragonimose (infection par des douves pulmonaires). Les signes et symptômes dépendent de l'organe touché et sont de sévérité variable. Certains patients peuvent être asymptomatiques."},"de":{"name":"Distomatose","definition":"Eine seltene Gruppe von parasitären Erkrankungen, die durch eine Infektion mit Egeln mit oralen und ventralen Saugnäpfen gekennzeichnet ist und Clonorchiasis (Infektion mit Leberegeln), Fasciolopsiasis (Infektion mit Darmegeln) und Paragonimiasis (Infektion mit Lungenegeln) umfasst. Die Anzeichen und Symptome hängen vom betroffenen Organ ab und sind unterschiedlich stark ausgeprägt. Einige Patienten können asymptomatisch sein."},"es":{"name":"Distomatosis","synonyms":["Distomiasis","Infección por tremátodos"],"definition":"Es un grupo de enfermedades parasitarias poco frecuentes caracterizadas por infección por trematodos con ventosa oral y ventral, que comprende la clonorquiasis (infección por trematodos hepáticos), la fasciolopsiasis (infección por trematodos intestinales) y la paragonimiasis (infección por trematodos pulmonares). Los signos y síntomas dependen del órgano afectado y son de gravedad variable. Algunos pacientes permanecen asintomáticos."},"it":{"name":"Distomatosi","synonyms":["Distomiasi","Infezione da Fasciola Hepatica"]},"nl":{"name":"Distomatose","synonyms":["Distomiasis","Infectie door Trematoda"],"definition":"Een groep van zeldzame parasitaire ziekten, gekenmerkt door infectie door trematoden met orale en ventrale zuignappen, bestaande uit Clonorchiasis (infectie door leverbotten), Fasciolopsiasis (infectie door darmbotten), en Paragonimiasis (infectie door longbotten). Verschijnselen en symptomen zijn afhankelijk van het aangetaste orgaan, en de ernst ervan is variabel. Sommige patiënten kunnen asymptomatisch zijn."},"pt":{"name":"Distomatose","synonyms":["Distomiase","Infeção por vermes parasitas"],"definition":"Grupo de doenças parasitárias raras caracterizadas por infeção por vermes com ventosas orais e ventrais, englobando a clonorquíase (infeção por vermes do fígado), Fasciolopsiase (infeção por vermes intestinais) e paragonimíase (infeção por vermes pulmonares). Os sinais e sintomas dependem do órgão afetado e são de gravidade variável. Alguns doentes podem ser assintomáticos."},"pl":{"name":"Przywrzyca","synonyms":["Choroba motylicza","Zakażenie przywrami","Dystomatoza"],"definition":"Grupa rzadkich chorób pasożytniczych związanych z zakażeniem przywrami z przyssawkami ustnymi i brzusznymi, obejmująca klonorchozę (zakażenie przywrami wątrobowymi), fasciolopsjozę (zakażenie przywrami jelitowymi) i paragonimoza (zakażenie przywrami płucnymi). Objawy zależą od zajętego narządu i mają różny stopień nasilenia. Niektórzy pacjenci mogą nie mieć objawów chorobowych."},"cs":{"name":"Distomatóza","synonyms":["Distomóza","Infekce motolicí"]},"uk":{"name":"Дистоматоз","synonyms":["Дистоміаз","Зараження гельмінтами"],"definition":"A rare group of infectious disease characterized by the infection of different organs (liver, lungs, or intestines) by flat worms live in contact with epitheliums. Clinical symptoms vary depending on the infected organ. In liver infection, (often presents with inflammation and obstruction of the biliary ducts) fever, allergic reactions (dermographism), abdominal pain, nausea, diarrhoea, hypereosinophilia and angiocholitis attacks can be observed. In lung infection, tuberculosis-like clinical signs (cough or haemoptysis) are observed without fever, however erratic cases may also exist. In intestine infection, painful diarrhea, abdominal pain, oedema (face, abdomen or legs), vomiting, anorexia, or intestinal obstruction can be observed, some patients can also be asymptomatic."},"zh":{"name":"双盘吸虫病","synonyms":["吸虫感染"]},"tr":{"name":"Distomatoz","synonyms":["Distomiyaz","Fluke enfeksiyonu"]}},"xrefs":[{"source":"ICD-10","code":"B66.0","qualifier":"BTNT","icd_relation":"inclusion","validated":true},{"source":"ICD-10","code":"B66.1","qualifier":"BTNT","icd_relation":"inclusion","validated":true},{"source":"ICD-10","code":"B66.2","qualifier":"BTNT","icd_relation":"inclusion","validated":true},{"source":"ICD-10","code":"B66.3","qualifier":"BTNT","icd_relation":"inclusion","validated":true},{"source":"ICD-10","code":"B66.4","qualifier":"BTNT","icd_relation":"inclusion","validated":true},{"source":"ICD-10","code":"B66.5","qualifier":"BTNT","icd_relation":"inclusion","validated":true},{"source":"ICD-10","code":"B66.8","qualifier":"NTBT","icd_relation":"inclusion","validated":true},{"source":"ICD-11","code":"1F80","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"918986134"},{"source":"ICD-11","code":"1F83","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"830824191"},{"source":"ICD-11","code":"1F85","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"1422824299"},{"source":"MONDO","code":"0015675","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"15675","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0040820","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"1891","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":68416,"name":"Rare infectious disease"},"parents":[{"orpha":163588,"name":"Rare parasitic disease","classifications":[203]}],"children":[{"orpha":658917,"name":"Clonorchiasis","type":"Disease"},{"orpha":658909,"name":"Fasciolopsiasis","type":"Disease"},{"orpha":658913,"name":"Paragonimiasis","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}