{"orpha":166421,"name":"Orgasm-induced epilepsy","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"A rare reflex epilepsy characterized by complex partial seizures with or without secondary generalization, or idiopathic primarily generalized epilepsy, triggered by sexual orgasm. Seizures usually start immediately, shortly after or a few hours after the achievement of orgasm, last a few seconds or minutes, and are followed, in very rare cases, by intense migraine.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-166421/","orphanet_url":"https://www.orpha.net/en/disease/detail/166421","names":{"fr":{"name":"Epilepsie induite par l'orgasme","definition":"Les crises induites par l'orgasme sont une maladie neurologique rare caractérisée par des convulsions partielles complexes avec ou sans généralisation secondaire, ou par une épilepsie idiopathique principalement généralisée, déclenchées par un orgasme. Habituellement, les crises débutent immédiatement, peu de temps après ou quelques heures après la fin de l'orgasme. Elles durent de quelques secondes à quelques minutes, et dans de très rares cas, elles sont suivies par une migraine intense."},"de":{"name":"Krampfanfälle, Orgasmus-induzierte","definition":"Eine seltene neurologische Erkrankung, die durch komplexe partielle Anfälle mit oder ohne sekundäre Generalisierung oder idiopathische primär generalisierte Epilepsie, ausgelöst durch einen sexuellen Orgasmus, gekennzeichnet ist. Die Anfälle beginnen in der Regel sofort, kurz nach oder einige Stunden nach dem Erreichen des Orgasmus, dauern einige Sekunden oder Minuten und werden, in sehr seltenen Fällen, von einer intensiven Migräne gefolgt."},"es":{"name":"Crisis epilépticas inducidas por el orgasmo","definition":"Es una epilepsia refleja poco frecuente caracterizada por convulsiones parciales complejas con o sin generalización secundaria desencadenada por el orgasmo sexual. Por lo habitual, las convulsiones comienzan de inmediato, poco después o unas pocas horas después de haber alcanzado el orgasmo, duran unos segundos o minutos, y son seguidas, en casos muy raros, por una migraña intensa."},"it":{"name":"Epilessia indotta dall'orgasmo","definition":"Le convulsioni indotte dall'orgasmo sono una malattia neurologica rara, caratterizzata da crisi epilettiche parziali complesse, con o senza generalizzazione secondaria, oppure da epilessia generalizzata idiopatica primaria, scatenate dall'orgasmo sessuale. Di solito le crisi iniziano immediatamente, poco dopo o qualche ora dopo il raggiungimento dell'orgasmo, durano qualche secondo o minuto e sono seguite, in casi molto rari, da emicrania intensa."},"nl":{"name":"Orgasmegeïnduceerde epilepsie","synonyms":["Epileptische aanval door orgasme","Insult door orgasme"],"definition":"Een zeldzame reflexepilepsie, gekenmerkt door complexe partiële insulten met of zonder secundaire generalisatie, of idiopathische primair gegeneraliseerde epilepsie, uitgelokt door seksueel orgasme. Insulten starten meestal onmiddellijk, kort of enkele uren na het bereiken van een orgasme, duren enkele seconden of minuten, en worden in zeer zeldzame gevallen gevolgd door intense migraine."},"pt":{"name":"Convulsões induzidas pelo orgasmo"},"pl":{"name":"Padaczka wywołana orgazmem"},"cs":{"name":"Záchvaty vyvolané orgasmem"},"uk":{"name":"Епілепсія з рефлекторними судомами, повязаними з оргазмом","definition":"Orgasm-induced seizures is a rare neurologic disease characterized by complex partial seizures with or without secondary generalization, or idiopathic primarily generalized epilepsy, triggered by sexual orgasm. Seizures usually start immediately, shortly after or a few hours after the achievement of orgasm, last a few seconds or minutes, and are followed, in very rare cases, by intense migraine."},"zh":{"name":"性高潮诱发的惊厥","definition":"性高潮诱导性惊厥是一种罕见的神经系统疾病，其特征是复杂性局部癫痫发作伴或不伴次级泛化，或由性高潮引起的原发性全身性癫痫。癫痫发作通常在达到性高潮后不久或几小时后立即开始，持续几秒或几分钟，在少数病例中，随后发生剧烈偏头痛。"},"tr":{"name":"Orgazm kaynaklı nöbetler"}},"xrefs":[{"source":"ICD-10","code":"G40.5","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"8A61.40","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"551362699"},{"source":"MONDO","code":"0015646","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4706598","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":310,"name":"Reflex epilepsy","classifications":[156,181]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":7.0,"area":"Worldwide","status":"Validated","source":"17201724[PMID]_27057393[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"17201724[PMID]_27057393[PMID]_ORPHANET"}],"phenotypes":null}