{"orpha":166418,"name":"Eating reflex epilepsy","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Eating epilepsy","Eating seizures"],"definition":"A rare reflex epilepsy characterized by in most cases complex partial seizures triggered by different components of eating, such as the sight of food, proprioceptive, olfactory or gustatory sensations, chewing, salivation, and gastric distension after food intake. The seizures may be idiopathic or associated with symptomatic localization-related epilepsies.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-166418/","orphanet_url":"https://www.orpha.net/en/disease/detail/166418","names":{"fr":{"name":"Epilepsie de l'alimentation","definition":"Épilepsie réflexe rare caractérisée, dans la plupart des cas, par des crises partielles complexes déclenchées par différents stimuli liés à l'alimentation, tels que la vue des aliments, les sensations proprioceptives, olfactives ou gustatives, la mastication, la salivation et la distension gastrique après ingestion de nourriture. Les convulsions peuvent être idiopathiques ou associées à des crises épileptiques focales symptomatiques."},"de":{"name":"Ess-Reflexepilepsie","synonyms":["Ess-Epilepsie","Ess-Krampfanfälle"],"definition":"Eine seltene Reflexepilepsie, die in den meisten Fällen durch komplexe partielle Anfälle gekennzeichnet ist, die durch verschiedene Komponenten des Essens ausgelöst werden, z. B. durch den Anblick von Lebensmitteln, propriozeptive, olfaktorische oder gustatorische Empfindungen, Kauen, Speichelfluss und Magendehnung nach der Nahrungsaufnahme. Die Anfälle können idiopathisch sein oder mit symptomatischen lokalisationsbezogenen Epilepsien einhergehen."},"es":{"name":"Epilepsia refleja de la alimentación","synonyms":["Crisis por la ingesta de alimentos","Epilepsia por la ingesta de alimentos"],"definition":"Es una epilepsia refleja poco frecuente caracterizada en la mayoría de los casos por crisis parciales complejas desencadenadas por diferentes componentes del proceso de la alimentación, tales como la visión de los alimentos, las sensaciones propioceptivas, olfativas o gustativas, la masticación, la salivación y la distensión gástrica después de la ingesta de alimentos. Las crisis pueden ser idiopáticas o asociadas a epilepsias focales sintomáticas."},"it":{"name":"Epilessia riflessa da assunzione di cibo","definition":"Si tratta di un'epilessia riflessa rara caratterizzata, nella maggior parte dei pazienti, da crisi parziali complesse, scatenate da diversi fattori collegati all'assunzione di cibo, che comprendono la vista del cibo, le sensazioni propriocettive, olfattive o gustative, la masticazione, la salivazione e la distensione gastrica che segue l'assunzione di cibo. Le crisi epilettiche possono essere idiopatiche o associate ad epilessie sintomatiche correlate alla localizzazione."},"nl":{"name":"Voedingsgeïnduceerde reflexepilepsie","synonyms":["Voedingsgeïnduceerde epilepsie","Voedingsgeïnduceerde epileptische aanvallen"],"definition":"Een zeldzame reflexepilepsie, in de meeste gevallen gekarakteriseerd door complexe partiële insulten uitgelokt door verschillende elementen van voeding, zoals uitzicht van het voedsel, proprioceptieve, olfactorische of gustatoire sensaties, kauwen, speekselvorming, en maagdistensie na inname van voedsel. De insulten kunnen idiopathisch zijn, of geassocieerd zijn met symptomatische lokalisatiegebonden epilepsieën."},"pt":{"name":"Convulsões alimentares"},"pl":{"name":"Napady padaczkowe wyzwalane jedzeniem","synonyms":["Eating epilepsy","Eating seizures"]},"cs":{"name":"Záchvaty vyvolané jídlem","synonyms":["Eating epilepsy","Eating seizures"]},"uk":{"name":"Епілепсія з рефлекторними судомами, повязаними зі споживанням їжі","synonyms":["Харчова епілепсія","Харчові напади"],"definition":"A rare reflex epilepsy characterized by in most cases complex partial seizures triggered by different components of eating, such as the sight of food, proprioceptive, olfactory or gustatory sensations, chewing, salivation, and gastric distension after food intake. The seizures may be idiopathic or associated with symptomatic localization-related epilepsies."},"zh":{"name":"进食反射性癫痫","synonyms":["进餐性惊厥"],"definition":"一种罕见的反射性癫痫，其特征是多数情况下由进食的不同方面引起的复杂性局部癫痫发作，如看到食物、本体感觉、嗅觉或味觉、咀嚼、流涎和进食后胃扩张。癫痫发作可能是特发性的，也可能与症状性定位相关癫痫有关。"},"tr":{"name":"Yemek yeme epilepsisi","synonyms":["Yemek yeme epilepsisi","Yeme nöbetleri"]}},"xrefs":[{"source":"ICD-10","code":"G40.5","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"8A61.40","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"91977543"},{"source":"MONDO","code":"0015645","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0393725","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":310,"name":"Reflex epilepsy","classifications":[156,181]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.5,"area":"Worldwide","status":"Validated","source":"Source: 33080481[PMID]_27986877[PMID]_ORPHANET"}],"phenotypes":null}