{"orpha":165958,"name":"Cavitary myiasis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Cavitary myiasis is a rare parasitic disease characterized by the infestation of natural body cavities (e.g. aural, nasal, oral, urogenital myiasis) and internal organs (e.g. cerebral myiasis, ophthalmomyiasis, intestinal and tracheopulmonary myiasis) with dipteran larvae. Clinical presentation is variable depending on the affected site(s) and degree of infestation and include foreign-body sensation (with or without movement sensation), hemorrhage, pain, edema, sensory loss, malodor, and pruritus, among others. Neurological features (e.g. motor deficits, seizures, reduced mental status, extrapyramidal signs) have been reported in cerebral myiasis.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-165958/","orphanet_url":"https://www.orpha.net/en/disease/detail/165958","names":{"fr":{"name":"Myiase des cavités","definition":"Une maladie parasitaire rare caractérisée par l'infestation des cavités naturelles du corps (myiase auriculaire, nasale, buccale, uro-génitale) et des organes internes (myiase cérébrale, ophtalmique, intestinale et trachéo-pulmonaire) par des larves de diptère. La présentation clinique varie selon le/les site(s) affecté(s) et le degré d'infestation, et inclut la sensation de présence d'un corps étranger (avec ou sans sensation de mouvement), une hémorragie, une douleur, un oedème, une perte sensorielle, une mauvaise odeur et un prurit, entre autres. Des signes neurologiques (comme des troubles moteurs, des convulsions, une diminution de l'état mental, des signes extrapyramidaux) ont été rapportés dans la myiase cérébrale."},"de":{"name":"Kavitarmyiasis","synonyms":["Körperhöhlen-Myiasis"],"definition":"Die Kavitarmyiasis ist eine seltene parasitäre Erkrankung, die durch den Befall natürlicher Körperhöhlen (z. B. aurale, nasale, orale, urogenitale Myiasis) und innerer Organe (z. B. zerebrale Myiasis, Ophthalmomyiasis, intestinale und tracheopulmonale Myiasis) mit Dipterenlarven (Larven zweiflügliger Insekten) veruracht ist. Die klinische Präsentation ist je nach betroffener(n) Stelle(n) und Grad des Befalls variabel und umfasst u. a. Fremdkörpergefühl (mit oder ohne Bewegungsempfindung), Blutungen, Schmerzen, Ödeme, Sensibilitätsverlust, Geruchsbelästigung und Pruritus. Neurologische Merkmale (z. B. motorische Defizite, Krampfanfälle, reduzierter mentaler Status, extrapyramidale Zeichen) wurden bei zerebraler Myiasis berichtet."},"es":{"name":"Miasis cavitaria","definition":"Es una enfermedad parasitaria poco frecuente, caracterizada por la infestación, por larvas de dípteros, de cavidades naturales del cuerpo (por ejemplo, miasis auditiva, nasal, oral, urogenital) y de órganos internos (por ejemplo, miasis cerebral, oftalmomiasis, miasis intestinal y traqueopulmonar). La presentación clínica es variable según los sitios afectados y el grado de infestación, e incluye sensación de cuerpo extraño (con o sin sensación de movimiento), hemorragia, dolor, edema, pérdida sensorial, mal olor y prurito, entre otros. En los casos de miasis cerebral, también se han notificado características neurológicas (por ejemplo, deficiencias motoras, convulsiones, estado mental reducido, signos extrapiramidales)."},"it":{"name":"Miasi cavitaria","definition":"La miasi cavitaria è una parassitosi rara caratterizzata dall'infestazione delle cavità naturali del corpo (miasi auricolare, nasale, orale e urogenitale) e degli organi interni (miasi cerebrale, oftalmomiasi, miasi intestinale e tracheopolmonare) da parte di larve di ditteri. Il quadro clinico è variabile e dipende dalla localizzazione (o dalle localizzazioni) e dal grado di infestazione; i segni clinici comprendono la sensazione di un corpo estraneo (con o senza sensazione di movimento), le emorragie, il dolore, l'edema, la perdita sensoriale, il cattivo odore e il prurito. Nei pazienti affetti da miasi cerebrale sono stati osservati sintomi neurologici (deficit motori, crisi epilettiche, riduzione delle prestazioni mentali e segni extrapiramidali)."},"nl":{"name":"Cavitaire myiasis","definition":"Cavitaire myiasis is een zeldzame parasitaire ziekte die gekarakteriseerd wordt door de besmetting van natuurlijke lichaamsholten (e.g. aurale, nasale, orale, urogenitale myiasis) en inwendige organen (e.g. cerebrale myiasis, oftalmomyiasis, intestinale en tracheopulmonale myiasis) met larven van Diptera (tweevleugeligen). Het klinisch beeld is variabel en hangt af van de getroffen plaats(en) en de mate van besmetting, en omvat onder andere vreemd voorwerp-gevoel (met of zonder bewegingsgevoel), hemorragie, pijn, oedeem, zintuiglijk verlies, onaangename lichaamsgeur, en pruritus. Neurologische kenmerken (e.g. motorische beperkingen, insulten, verminderde mentale toestand, extrapiramidale tekenen) werden reeds gerapporteerd bij cerebrale myiasis."},"pt":{"name":"Miíase cavitária"},"pl":{"name":"Muszyca jamy ciała"},"cs":{"name":"Kavitární myiáze"},"uk":{"name":"Кавернозний міаз","definition":"Cavitary myiasis is a rare parasitic disease characterized by the infestation of natural body cavities (e.g. aural, nasal, oral, urogenital myiasis) and internal organs (e.g. cerebral myiasis, ophthalmomyiasis, intestinal and tracheopulmonary myiasis) with dipteran larvae. Clinical presentation is variable depending on the affected site(s) and degree of infestation and include foreign-body sensation (with or without movement sensation), hemorrhage, pain, edema, sensory loss, malodor, and pruritus, among others. Neurological features (e.g. motor deficits, seizures, reduced mental status, extrapyramidal signs) have been reported in cerebral myiasis."},"zh":{"name":"空洞性蝇蛆病","definition":"腔性蝇蛆病是一种罕见的寄生虫病，其特征是自然体腔(如耳、鼻、口、泌尿生殖器蝇蛆病)和内脏(如脑蝇蛆病病、眼蝇蛆病、肠蝇蛆病和气管肺蝇蝇蛆病)被双翅类幼虫感染。临床表现因受累部位和感染程度而异，包括异物感(伴或不伴运动感)、出血、疼痛、水肿、感觉丧失、异味和瘙痒等。神经系统特征(如运动障碍、惊厥、精神状态下降、锥体外系体征)已在脑蝇蛆病中被报道。"},"tr":{"name":"Kaviter miyazi"}},"xrefs":[{"source":"ICD-10","code":"B87.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"1G01.0","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"1105275196"},{"source":"ICD-11","code":"1G01.1","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"615179438"},{"source":"ICD-11","code":"1G01.2","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"1171166323"},{"source":"ICD-11","code":"1G01.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"710669091"},{"source":"MONDO","code":"0015623","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4707154","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":68416,"name":"Rare infectious disease"},"parents":[{"orpha":75110,"name":"Myiasis","classifications":[203]},{"orpha":716348,"name":"Rare isolated progressive predominantly chorioretinal disorder","classifications":[189]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"28822697[PMID]_ORPHANET"}],"phenotypes":null}