{"orpha":139423,"name":"Idiopathic acute transverse myelitis","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":[],"definition":"A rare immune-mediated inflammatory demyelinating disorder of the spinal cord with motor, sensory and autonomic involvement.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-139423/","orphanet_url":"https://www.orpha.net/en/disease/detail/139423","names":{"fr":{"name":"Myélite transverse aiguë idiopathique","definition":"La myélite transverse aiguë (MTA) idiopathique est une maladie immunitaire inflammatoire démyélinisante de la moelle épinière qui présente des manifestations motrices, sensitives et autonomiques."},"de":{"name":"Myelitis, akute transverse, idiopathische","definition":"Die Idiopathische akute transverse Myelitis (ATM) ist eine immunvermittelte, entzündliche, demyelinisierende Erkrankung des Rückenmarks mit motorischer, sensorischer und vegetativer Beteiligung."},"es":{"name":"Mielitis transversa aguda idiopática","definition":"Es un trastorno desmielinizante inflamatorio de mediación inmunológica de la médula espinal con afectación motora, sensorial y autónoma."},"it":{"name":"Mielite trasversa acuta idiopatica"},"nl":{"name":"Idiopathische acute transversale myelitis","definition":"Een zeldzame immuungemedieerde inflammatoire demyeliniserende aandoening van ruggenmerg met motorische, sensorische en autonome betrokkenheid."},"pt":{"name":"Mielite transversa aguda idiopática","definition":"Mielite transversa aguda idiopática (ATM) é uma doença inflamatória desmielinizante mediada pelo sistema imunitário da espinal medula com envolvimento motor, sensorial e autónomo."},"pl":{"name":"Idiopatyczne ostre poprzeczne zapalenie rdzenia","synonyms":["ATM/TM"]},"cs":{"name":"Idiopatická akutní transverzální myelitida","synonyms":["ATM/TM"]},"uk":{"name":"Ідіопатичний гострий поперечний мієліт","definition":"A rare immune-mediated inflammatory demyelinating disorder of the spinal cord with motor, sensory and autonomic involvement."},"zh":{"name":"特发性急性横贯性脊髓炎","synonyms":["急性横贯性脊髓炎/横贯性脊髓炎"],"definition":"一种罕见的免疫介导的脊髓炎性脱髓鞘疾病，伴运动、感觉和自主神经受累。"},"tr":{"name":"İdiyopatik akut transvers miyelit","synonyms":["ATM/TM"]}},"xrefs":[{"source":"ICD-10","code":"G37.3","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"8A41.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0015344","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1719404","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":139417,"name":"Acute transverse myelitis","classifications":[181]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.25,"area":"Europe","status":"Validated","source":"[EXPERT]"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"[EXPERT]"}],"phenotypes":null}