{"orpha":137871,"name":"OBSOLETE: Laminopathy type Decaudain-Vigouroux","type":"Disease","group":"Disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":["OBSOLETE: Laminopathy with severe metabolic syndrome and myopathy"],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Familial partial lipodystrophy, Dunnigan type","url":"https://raremap.alftech.space/d/ORPHA-137871/","orphanet_url":"https://www.orpha.net/en/disease/detail/137871","names":{"fr":{"name":"OBSOLETE : Laminopathie type Decaudain-Vigouroux","synonyms":["OBSOLETE : Laminopathie avec syndrome métabolique sévère et myopathie"]},"de":{"name":"OBSOLET: Laminopathie Typ Decaudain-Vigouroux","synonyms":["OBSOLET: Laminopathie mit schwerem metabolischen Syndrom und Myopathie"]},"es":{"name":"OBSOLETO: Laminopatía tipo Decaudain-Vigouroux","synonyms":["OBSOLETO: Laminopatía con síndrome metabólico grave y miopatía"]},"it":{"name":"OBSOLETO: Laminopatia tipo Decaudain-Vigouroux","synonyms":["OBSOLETO: Laminopatia con sindrome metabolica grave e miopatia"]},"nl":{"name":"OBSOLEET: Laminopathie type Decaudain-Vigouroux","synonyms":["OBSOLEET: Laminopathie met ernstig metabool syndroom en myopathie"]},"pt":{"name":"OBSOLETO: Laminopatia, tipo Decaudain-Vigouroux","synonyms":["OBSOLETO: Laminopatia com síndrome metabólico grave e miopatia"]},"pl":{"name":"NIEAKTUALNE: Laminopatia typu Decaudaina i Vigouroux","synonyms":["NIEAKTUALNE: Laminopatia z ciężkim zespołem metabolicznym i miopatią"]},"cs":{"name":"NEAKTUÁLNÍ: Laminopatie, typ Decaudainové-Vigourouxové","synonyms":["NEAKTUÁLNÍ: Laminopatie s těžkým metabolickým syndromem a myopatií","NEAKTUÁLNÍ: Laminopatie, typ Decaudain-Vigourouxové"]},"uk":{"name":"ЗАСТАРІЛО: Ламінопатія типу Декадена-Вігуру","synonyms":["ЗАСТАРІЛО: Ламінопатія з тяжким метаболічним синдромом та міопатією"]},"zh":{"name":"弃用：Decaudain Vigouroux型核纤层蛋白病","synonyms":["核纤层蛋白病伴有严重代谢综合征和肌病"]},"tr":{"name":"Eski adı: Laminopati tipi Decaudain-Vigouroux","synonyms":["Ağır metabolik sendrom ve miyopatili laminopati"]}},"xrefs":[],"associations":[{"type":"Referred to","orpha":2348,"name":"Familial partial lipodystrophy, Dunnigan type"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}