{"orpha":100021,"name":"Primary plasmacytoma of the bone","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This disease is described under Plasmacytoma","url":"https://raremap.alftech.space/d/ORPHA-100021/","orphanet_url":"https://www.orpha.net/en/disease/detail/100021","names":{"fr":{"name":"Plasmacytome primaire de l'os"},"de":{"name":"Plasmozytom, primäres, des Knochens"},"es":{"name":"Plasmacitoma primario del hueso"},"it":{"name":"Plasmocitoma primario dell'osso"},"nl":{"name":"Primair plasmacytoom van bot"},"pt":{"name":"Plasmacitoma primário do osso"},"pl":{"name":"Pierwotny szpiczak mnogi kości"},"cs":{"name":"Primární plazmocytom kosti"},"uk":{"name":"Первинна плазмоцитома кістки"},"zh":{"name":"骨原发性浆细胞瘤"},"tr":{"name":"Kemiğin primer plazmasitomu"}},"xrefs":[{"source":"ICD-10","code":"C90.3","qualifier":"E","icd_relation":"specific","validated":true},{"source":"ICD-11","code":"2A83.2","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1163480196"},{"source":"MONDO","code":"0015042","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":86855,"name":"Plasmacytoma","classifications":[181,194,202,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.15,"area":"United States","status":"Validated","source":"19016727[PMID]_SEER Surveillance Epidemiology and End Results 1992-2004[OTHER]"}],"phenotypes":null}