Secondary pulmonary hemosiderosis
- Type
- Disease
- Group
- Disorder
- Status
- active
Secondary pulmonary hemosiderosis is a respiratory disease due to the deposition of hemosiderin-laden macrophages in lungs as a result of repeated alveolar hemorrhage secondary to another disease, especially dysimmunitary disorders (i.e. Heiner syndrome, autoimmune diseases), thrombotic disorders and cardiovascular disorders such as mitral stenosis. It manifests as a triad of hemoptysis, anemia and diffuse parenchymal infiltrates on chest radiography
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Secondary pulmonary hemosiderosis | |
| fr | Hémosidérose pulmonaire secondaire | |
| de | Lungen-Hämosiderose, sekundäre | |
| es | Hemosiderosis pulmonar secundaria | |
| it | Emosiderosi polmonare secondaria | |
| nl | Secundaire pulmonale hemosiderose | |
| pt | Hemossiderose pulmonar, secundária | |
| pl | Wtórna hemosyderoza płuc | |
| cs | Sekundární plicní hemosideróza | |
| uk | Вторинний гемосидероз легень | |
| zh | 继发性肺含铁血黄素沉积 | |
| tr | Sekonder pulmoner hemosideroz |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | E83.1+ | NTBT | attributed | validated |
| ICD-10 | J99.8* | NTBT | attributed | validated |
| ICD-11 | CB05.5 | E | specific | validated |
| MONDO | 0020553 | E | validated | |
| UMLS | C4274326 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:264944Secondary interstitial lung disease in childhood and adulthood
rare respiratory diseases; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/99930
- This record as JSON: /data/d/99930.json