Theca steroid-producing cell malignant tumor of ovary, not further specified
Synonyms: Theca (steroid-producing) cell cancer, not further specified
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adult
- Status
- active
A rare malignant sex cord stromal tumor of ovary of unknown histological lineage, occurring in adult women, characterized, in most cases, by manifestations of androgen excess (hirsutism, hair loss, amenorrhea, or oligomenorrhea) and, occasionally, Cushing syndrome.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Theca steroid-producing cell malignant tumor of ovary, not further specified | Theca (steroid-producing) cell cancer, not further specified |
| fr | Tumeur maligne à cellules stéroïdiennes de l'ovaire sans autre précision | Cancer à cellules stéroïdiennes sans autre précision |
| de | Steroid-produzierender maligner Thekazelltumor, nicht klassifizierter | Thekazellkarzinom (Steroid-produzierend), nicht klassifiziert |
| es | Tumor maligno de las células esteroideas del ovario, sin especificar | Cáncer de células tecales (productoras de esteroides), sin más especificaciones |
| it | Tumore maligno delle cellule della teca dell'ovaio steroido-producenti, non altrimenti specificato | Cancro delle cellule della teca (steroido-producenti), non altrimenti specificato |
| nl | Maligne steroïdeproducerende thecaceltumor van ovarium, niet verder gespecifieerd | Kwaadaardige steroïdeproducerende thecaceltumor van eierstok, niet verder gespecifieerd · Thecacelkanker (steroïdeproducerend), niet verder gespecifieerd |
| pt | Tumor de células da teca (produtor de esteróides), não especificado | |
| pl | Theca steroid-producing cell malignant tumor of ovary, not further specified | = en |
| cs | Dále nespecifikovaný maligní nádor ovaria s produkcí steroidů z thekálních buněk | Dále nespecifikovaná rakovina z thekálních buněk produkujících steroidy |
| uk | Злоякісна пухлина яєчника з стероїдпродукуючими клітинами Тека, не уточнена | Тека (стероїдопродукуючий) клітинний рак, не уточнено |
| zh | 卵巢激素合成性卵泡膜细胞恶性肿瘤未指定类型 | 卵泡膜(产生类固醇)细胞癌未指定型 |
| tr | Teka steroid üreten habis hücreli over tümörü-tam tanımlanmamış | Teka (steroid üreten) hücreli kanser, daha fazla belirtilmemiş |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C56 | NTBT | attributed | validated |
| ICD-11 | 2C73.Y | NTBT | index | validated |
| MONDO | 0020543 | E | validated | |
| UMLS | C4274494 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:35808Malignant sex cord stromal tumor of ovary
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | — | Europe | Class only | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/99917
- This record as JSON: /data/d/99917.json