raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:99870

OBSOLETE: Letterer-Siwe disease

inactive · referred to ORPHA:389Langerhans cell histiocytosis

Synonyms: OBSOLETE: Acute and disseminated Langerhans cell histiocytosis

Type
Clinical subtype
Group
Subtype of disorder
Status
inactive
Flag
Obsolete entity

This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Langerhans cell histiocytosis

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enOBSOLETE: Letterer-Siwe diseaseOBSOLETE: Acute and disseminated Langerhans cell histiocytosis
frOBSOLETE : Maladie de Letterer-SiweOBSOLETE : Histiocytose langerhansienne aiguë et disséminée
deOBSOLET: Letterer-Siwe-KrankheitOBSOLET: Langerhans-Zell-Histiozytose, akute und disseminierte
esOBSOLETO: Enfermedad de Letterer-SiweOBSOLETO: Histiocitosis de células de Langerhans aguda y diseminada
itOBSOLETO: Malattia di Letterer-SiweOBSOLETO: Istiocitosi acuta e disseminata a cellule di Langerhans
nlOBSOLEET: Ziekte van Letterer-SiweOBSOLEET: Acute en verspreide Langerhanscelhistiocytose
ptOBSOLETO: Doença de Letterer-Siwe
plNIEAKTUALNE: Choroba Letterera i SiwegoNIEAKTUALNE: Ostra i rozsiana histiocytoza z komórek Langerhansa
csNEAKTUÁLNÍ: Lettererova-Siweho chorobaNEAKTUÁLNÍ: Akutní a diseminovaná histiocytóza z Langerhansových buněk · NEAKTUÁLNÍ: Letterer-Siweho choroba
ukЗАСТАРІЛО: Хвороба Леттерера-СівеЗАСТАРІЛО: Гострий та дисемінований гістіоцитоз клітин Лангерганса
zh弃用:莱特勒-西韦病急性播散性朗格汉斯细胞组织细胞增生症
trEski adı: Letterer-Siwe hastalığıAkut ve yaygın Langerhans hücre histiyositozu
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card