ORPHA:99126

Congenital pulmonary vein atresia

Synonyms: CPVA · Congenital PVA

Orphadata ships no English definition for this code.

Names in Orphadata languages

12 of 12 languages

Lang	Name	Synonyms
en	Congenital pulmonary vein atresia	CPVA · Congenital PVA
fr	Atrésie congénitale des veines pulmonaires
de	Pulmonalvenenatresie, kongenitale	CPVA · Kongenitale PVA
es	Atresia congénita de la vena pulmonar	AVP congénita
it	Atresia congenita delle vene polmonari	CPVA · PVA congenita
nl	Congenitale atresie van vena pulmonalis	CPVA · Congenitale PVA · Congenitale atresie van longader
pt	Atresia congénita da veia pulmonar	CPVA · PVA congénita
pl	Atrezja zyly plucnej	Wrodzona atrezja żyły płucnej
cs	Vrozená atrézie plicní žíly	= en
uk	Вроджена атрезія легеневих вен	Вроджений PVA · CPVA
zh	弃用：肺静脉闭锁
tr	Eski adı: Pulmoner ven atrezisi

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
ICD-10	Q26.8	NTBT	attributed	validated
ICD-11	LA86.Y	NTBT	index	validated
MONDO	0957556	E		validated
UMLS	C0344679	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

ORPHA:3188Congenital pulmonary veins atresia or stenosis
rare developmental anomalies during embryogenesis; rare cardiac malformations; rare respiratory diseases; rare circulatory system diseases; rare transplant-related disorders

No children.

0 direct

Orphanet records no gene directly on this code.

0 records

No prevalence record in this release.

Orphanet has no HPO annotation for this code in this release.