Right inferior vena cava connecting to left-sided atrium
Synonyms: Right IVC connecting to left-sided atrium · Right inferior caval vein connecting to left-sided atrium
- Type
- Morphological anomaly
- Group
- Disorder
- Status
- active
A rare vascular anomaly characterized by a congenital anomalous connection between the inferior vena cava and the left atrium. Clinical manifestations depend on the presence and nature of additional cardiac defects and include cyanosis, dyspnea, failure to thrive, clubbing of fingers and toes, and potentially heart failure.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Right inferior vena cava connecting to left-sided atrium | Right IVC connecting to left-sided atrium · Right inferior caval vein connecting to left-sided atrium |
| fr | Drainage anormal de la veine cave inférieure dans l'oreillette gauche | |
| de | Rechte Vena cava inferior mit Mündung in den linken Vorhof | Rechte untere Hohlvene mit Mündung in den linken Vorhof |
| es | Vena cava inferior derecha conectada a la aurícula izquierda | VCI derecha conectada a la aurícula izquierda |
| it | Vena cava inferiore destra collegata all'atrio sinistro | |
| nl | Rechter vena cava inferior verbonden met linkeratrium | Rechter VCI verbonden met linkeratrium · Rechter onderste holle ader verbonden met linkeratrium |
| pt | VCI, direita, ligando ao lado esquerdo auricular | |
| pl | Prawa żyła główna dolna uchodząca do lewego przedsionka | Prawa IVC uchodząca do lewego przedsionka · Prawa żyła główna dolna łącząca się z lewostronnym przedsionkiem |
| cs | Pravá dolní dutá žíla ústící do levé síně | Pravá VCI napojující se na levostrannou síň · Pravá dolní dutá žíla napojujicí se na levostrannou síň |
| uk | Права нижня порожниста вена, яка дренується в ліворозташоване передсердя | Права нижня порожниста вена зєднується з лівим передсердям · Права вентрикулярна вена зєднується з лівим передсердям |
| zh | 右下腔静脉连接左心房 | 右侧下腔静脉连接左心房 |
| tr | Sol taraftaki atriyuma bağlanan sağ inferior vena kava | Sol taraftaki atriyuma bağlanan sağ IVC · Sol taraftaki atriyuma bağlanan sağ inferior kaval ven |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q26.8 | NTBT | attributed | validated |
| ICD-11 | LA86.Y | NTBT | attributed | validated |
| MONDO | 0020448 | E | validated | |
| UMLS | C3164330 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:95499Congenital anomaly of the inferior vena cava
rare developmental anomalies during embryogenesis; rare cardiac malformations; rare circulatory system diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/99119
- This record as JSON: /data/d/99119.json