raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:99118

Coronary sinus atresia

Type
Morphological anomaly
Group
Disorder
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enCoronary sinus atresia
frAtrésie du sinus coronaire
deKoronarsinusatresie
esAtresia del seno coronario
itAtresia del seno coronarico
nlCoronaire sinusatresie
ptAtresia do seio coronário
plAtrezja zatoki wieńcowej
csAtrézie koronárního sinu
ukАтрезія коронарного синуса
zh冠状静脉窦闭锁
trKoroner sinüs atrezisi
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10Q21.1NTBTattributedvalidated
ICD-11LA86.YBTNTindexvalidated
MONDO0020447Evalidated
UMLSC0344683Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card