Cor triatriatum dexter
Synonyms: Cor triatriatum dextrum · Divided right atrium
- Type
- Morphological anomaly
- Group
- Disorder
- Age of onset
- Adult, Childhood, Infancy
- Status
- active
A rare, congenital, non-syndromic, heart malformation characterized by the persistence of the embryonic right valve of the sinus venosus which results in a subdivision of right atrium into two chambers. Clinical manifestations depend on the degree of right atrial septation and the size of sinoatrial orifice and vary from asymptomatic to symptoms of tricuspid valve stenosis, atrial fibrillation, cyanosis, syncope, elevated central venous pressure and right heart failure. The anomaly may be isolated or associated with other congenital heart anomalies.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Cor triatriatum dexter | Cor triatriatum dextrum · Divided right atrium |
| fr | Coeur triatrial droit | Cor triatriatum dexter · Cor triatriatum dextrum · Division de l'atrium droit · Division de l'oreillette droite |
| de | Cor triatriatum dexter | Geteilter rechter Vorhof |
| es | Cor triatriatum dexter | Aurícula derecha dividida · Cor triatriatum dextrum |
| it | Cor triatriatum dexter | Atrio destro diviso · Cor triatriatum dextrum |
| nl | Cor triatriatum dexter | Cor triatriatum dextrum · Verdeeld rechteratrium |
| pt | Cor triatriatum destro | |
| pl | Serce trójprzedsionkowe prawe | Prawy przedsionek podzielony |
| cs | Cor triatriatum dexter | Cor triatriatum dextrum · Rozdělená pravá síň |
| uk | Трьохпередсердне серце (праве) | Cor triatriatum dextrum · Розділене праве передсердя |
| zh | 右侧三房心 | 右心房三间隔 |
| tr | Kor triatriatum dekster | Bölünmüş sağ atriyum · Kor triatriatum dekstrum |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q24.2 | NTBT | attributed | validated |
| ICD-11 | LA8F | NTBT | index | validated |
| MONDO | 0020429 | E | validated | |
| UMLS | C0344697 | E | validated | |
| GARD | 12483 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:1463Triatrial heart
rare developmental anomalies during embryogenesis; rare cardiac malformations
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/99098
- This record as JSON: /data/d/99098.json