raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:99069

OBSOLETE: Univentricular heart with single atrio-ventricular valve

inactive · referred to ORPHA:1464Univentricular heart

Type
Clinical subtype
Group
Subtype of disorder
Status
inactive
Flag
Obsolete entity

This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Univentricular heart

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enOBSOLETE: Univentricular heart with single atrio-ventricular valve
frOBSOLETE : Coeur univentriculaire à valve auriculoventriculaire unique
deOBSOLET: Univentrikuläres Herz mit singulärer atrio-ventrikulärer Klappe
esOBSOLETO: Corazón univentricular con una sola válvula ventricular
itOBSOLETO: Cuore monoventricolare con valvola atrio-ventricolare singola
nlOBSOLEET: Univentriculair hart met enkelvoudige atrioventriculaire klep
ptOBSOLETO: Coração univentricular com válvula auriculoventricular única
plNIEAKTUALNE: Serce jednokomorowe z pojedyńczą zastawką przedsionkowo-komorową
csNEAKTUÁLNÍ: Srdce se společnou komorou a jedinou AV chlopní
ukОдношлуночкове серце з єдиним атріо-вентрикулярним клапаном
zh单心室伴发单房室瓣
trTek atriyoventriküler kapaklı univentriküler kalp
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card