raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:99047

Double outlet right ventricle with doubly committed ventricular septal defect

inactive · moved to ORPHA:423693Double outlet right ventricle with subaortic or doubly committed ventricular septal defect

Type
Clinical subtype
Group
Subtype of disorder
Status
inactive
Flag
Deprecated entity

This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Double outlet right ventricle with subaortic or doubly committed ventricular septal defect

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enDouble outlet right ventricle with doubly committed ventricular septal defect
frVentricule droit à double issue avec communication interventriculaire sous-aortique et sous-pulmonaire
deRechter Doppelausstromventrikel mit double-committed Ventrikelseptumdefekt
esDoble salida ventricular derecha con comunicación interventricular doblemente comprometida
itVentricolo destro a doppia uscita con difetto del setto ventricolare doppiamente connesso
nlRechterventrikel met dubbele uitstroom met doubly-committed ventrikelseptumdefect
ptDupla saída do ventrículo direito com defeito do septo ventricular duplamente implicado
plDwuodpływowa prawa komora z ubytkiem przegrody międzykomorowej związanym z obydwoma naczyniami
csDvojvýtoková pravá komora s dvojitě umístěným defektem komorového septa
ukПодвійне відходження великих артерій від правого шлуночка з підартеріальним дефектом міжшлуночкової перетинки
zh右心室双出口合并双室间隔缺损
trÇift katlı ventriküler septal defektli çift çıkışlı sağ ventrikül
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
UMLSC0344644Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card