raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:99044

Double outlet right ventricle with subaortic ventricular septal defect

inactive · moved to ORPHA:423693Double outlet right ventricle with subaortic or doubly committed ventricular septal defect

Type
Clinical subtype
Group
Subtype of disorder
Status
inactive
Flag
Deprecated entity

This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Double outlet right ventricle with subaortic or doubly committed ventricular septal defect

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enDouble outlet right ventricle with subaortic ventricular septal defect
frVentricule droit à double issue avec communication interventriculaire sous-aortique
deRechter Doppelausstromventrikel mit subaortalem Ventrikelseptumdefekt
esDoble salida ventricular derecha con comunicación interventricular subaórtica
itVentricolo destro a doppia uscita con difetto del setto ventricolare subaortico
nlRechterventrikel met dubbele uitstroom met subaortaal ventrikelseptumdefect
ptDupla saída do ventrículo direito com defeito do septo ventricular subaórtico
plDwuodpływowa prawa komora z podaortalnym ubytkiem przegrody międzykomorowej
csDvojvýtoková pravá komora se subaortálním defektem komorového septa
ukПодвійне відходження магістральних судин від правого шлуночку з субаортальним чи подвійним дефектом міжшлуночкової перетинки
zh右心室双出口合并主动脉瓣下室间隔缺损
trSubaortik ventriküler septal defektli çift çıkışlı sağ ventrikül
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
UMLSC1956411Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card