raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:98535

Frontotemporal degeneration with dementia

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enFrontotemporal degeneration with dementia
frDégénérescence fronto-temporale avec démence
deFrontotemporale Degeneration mit Demenz
esDegeneración frontotemporal con demencia
itDegenerazione frontotemporale con demenza
nlFrontotemporale degeneratie met dementie
ptDemência com degeneração frontotemporal
plZwyrodnienie czołowo-skroniowe z otępieniem
csFrontotemporální degenerace s demencí
ukЛобно-скронева дегенерація з деменцією
zh额颞叶变性伴痴呆
trDemans ile seyreden frontotemporal dejenerasyon
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
UMLSC5681727Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (5):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card