ORPHA:98421
Primary acquired red cell aplasia
Synonyms: Primary autoimmune red cell aplasia
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary acquired red cell aplasia | Primary autoimmune red cell aplasia |
| fr | Aplasie primaire acquise de la lignée rouge | Aplasie primaire autoimmune de la lignée rouge |
| de | Primäre erworbene Aplasie der roten Blutkörperchen | Primäre autoimmune Aplasie der roten Blutkörperchen |
| es | Aplasia eritrocítica primaria adquirida | Aplasia de glóbulos rojos primaria adquirida · Aplasia eritrocítica primaria autoinmune |
| it | Aplasia eritrocitaria primitiva acquisita | Aplasia eritrocitaria autoimmune primitiva |
| nl | Primaire verworven erytrocytaire aplasie | Primaire auto-immune aplasie van rode bloedcel |
| pt | Aplasia primária adquirida dos glóbulos vermelhos | |
| pl | Pierwotna nabyta aplazja krwinek czerwonych | = en |
| cs | Aplázie červené krevní řady | = en |
| uk | Первинна набута еритроцитарна аплазія | Первинна аутоімунна еритроцитарна аплазія |
| zh | 红细胞再生障碍 | = en |
| tr | Kırmızı hücre aplazisi | = en |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0020113 | E | validated | |
| UMLS | C0034902 | E | validated | |
| MedDRA | 10038184 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:164823Rare acquired aplastic anemia
rare hematological diseases; rare transplant-related disorders
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Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/98421
- This record as JSON: /data/d/98421.json