raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:98421

Primary acquired red cell aplasia

Synonyms: Primary autoimmune red cell aplasia

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPrimary acquired red cell aplasiaPrimary autoimmune red cell aplasia
frAplasie primaire acquise de la lignée rougeAplasie primaire autoimmune de la lignée rouge
dePrimäre erworbene Aplasie der roten BlutkörperchenPrimäre autoimmune Aplasie der roten Blutkörperchen
esAplasia eritrocítica primaria adquiridaAplasia de glóbulos rojos primaria adquirida · Aplasia eritrocítica primaria autoinmune
itAplasia eritrocitaria primitiva acquisitaAplasia eritrocitaria autoimmune primitiva
nlPrimaire verworven erytrocytaire aplasiePrimaire auto-immune aplasie van rode bloedcel
ptAplasia primária adquirida dos glóbulos vermelhos
plPierwotna nabyta aplazja krwinek czerwonych= en
csAplázie červené krevní řady= en
ukПервинна набута еритроцитарна аплазіяПервинна аутоімунна еритроцитарна аплазія
zh红细胞再生障碍= en
trKırmızı hücre aplazisi= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO0020113Evalidated
UMLSC0034902Evalidated
MedDRA10038184Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (2):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card