ORPHA:98287
Histiocytic and dendritic cell tumor
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Histiocytic and dendritic cell tumor | |
| fr | Tumeur des histiocytes et des cellules dendritiques | |
| de | Histiozytischer und dendritischer Zell-Tumor | |
| es | Tumor de células histiocíticas y dentríticas | |
| it | Tumore delle cellule dendritiche e istiocitiche | |
| nl | Histiocytische en dendritische celtumor | |
| pt | Tumor de células histiocíticas e dendríticas | |
| pl | Guz z komórek histiocytarnych i dendrytycznych | |
| cs | Nádory z histiocytů a dendritických buněk | |
| uk | Гістіоцитарна та дендритноклітинна пухлина | |
| zh | 组织细胞和树突状细胞肿瘤 | |
| tr | Histiositik ve dendritik hücreli tümör |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0006247 | E | validated | |
| MONDO | 6247 | E | validated | |
| UMLS | C1334030 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:171898Lymphoid hemopathy
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | 0.05 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/98287
- This record as JSON: /data/d/98287.json