Straddling or overriding tricuspid valve
- Type
- Morphological anomaly
- Group
- Disorder
- Status
- active
Straddling or overriding tricuspid valve is a rare, congenital, tricuspid valve malformation characterized by the tricuspid valve that overrides the ventricular septum and communicates with both ventricles, as part of the tension apparatus of the valve crosses the ventricular septal defect and is attached in the left ventricle. The anomaly occurs with other congenital heart defects (transposition of great vessels, left ventricle outflow tract obstruction, double outlet right ventricle, hypoplastic right ventricle), which determine the main clinical manifestation.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Straddling or overriding tricuspid valve | |
| fr | Straddling ou overriding de la valve tricuspide | |
| de | Trikuspidalklappe, gespreizte und/oder reitende | |
| es | Cabalgamiento o superposición de la válvula tricúspide | |
| it | Valvola tricuspide "a cavallo" e/o "con sconfinamento" | |
| nl | Gespreide of overrijdende tricuspidalisklep | |
| pt | Válvula tricúspide, com straddling ou overriding | |
| pl | Wada zastawki trójdzielnej typu straddling (overriding ) | |
| cs | Vyklenutí nebo potlačení trikuspidální chlopně | |
| uk | Аномальне розташування хорд та площини трикуспідального клапана по відношенню до правого шлуночка | |
| zh | 三尖瓣重迭 | |
| tr | İki taraflı veya baskın triküspit kapak |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q22.8 | NTBT | attributed | validated |
| ICD-11 | LA87.0Y | BTNT | index | validated |
| MONDO | 0019814 | E | validated | |
| UMLS | C5761644 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:98721Congenital tricuspid malformation
rare developmental anomalies during embryogenesis; rare cardiac malformations
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/95461
- This record as JSON: /data/d/95461.json