raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:93209

OBSOLETE: Idiopathic steroid-sensitive nephrotic syndrome with diffuse mesangial proliferation

inactive · referred to ORPHA:69061Idiopathic steroid-sensitive nephrotic syndrome

Type
Histopathological subtype
Group
Subtype of disorder
Status
inactive
Flag
Obsolete entity

This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Idiopathic steroid-sensitive nephrotic syndrome

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enOBSOLETE: Idiopathic steroid-sensitive nephrotic syndrome with diffuse mesangial proliferation
frOBSOLETE : Syndrome néphrotique idiopathique corticosensible avec prolifération mésangiale diffuse
deOBSOLET: Nephrotisches Syndrom, idiopathisches steroid-sensitives, mit diffuser mesangialer Proliferation
esOBSOLETO: Síndrome nefrótico idiopático sensible a esteroides con proliferación mesangial difusa
itOBSOLETO: Sindrome nefrosica idiopatica steroido-sensibile con proliferazione mesangiale diffusa
nlOBSOLEET: Idiopathisch steroïdegevoelig nefrotisch syndroom met diffuse mesangiale proliferatie
ptOBSOLETO: Síndrome nefrótico idiopático com proliferação mesangial difusa, sensível aos esteróides
plNIEAKTUALNE: Steroidowrazliwy idiopatyczny zespól nerczycowy z rozlana proliferacja mezangium
csNEAKTUÁLNÍ: Idiopatický nefrotický na steroidy citlivý syndrom s difuzní proliferací mesangia
ukЗАСТАРІЛО: Ідіопатичний стероїдочутливий нефротичний синдром з дифузною мезангіальною проліферацією
zh弃用:激素敏感型原发性肾病综合征伴弥漫性系膜增生
trEski adı: Yaygın mezangial proliferasyon ile seyreden idiyopatik steroide duyarlı nefrotik sendrom
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card