raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:90066

Pneumonia caused by Pseudomonas aeruginosa infection

Type
Particular clinical situation in a disease or syndrome
Group
Disorder
Inheritance
Not applicable
Age of onset
All ages
Status
active

A rare pulmonary disease characterized by primary or nonbacteremic pneumonia most frequently arising in an intensive care setting, or bacteremic pneumonia, which is typically associated with neutropenia. Chronic lower respiratory tract infection with development of episodes of pneumonia is common in patients with cystic fibrosis. Acute infections are potentially life-threatening. Patients present with fever, chills, dyspnea, cyanosis, productive cough, as well as signs of severe systemic toxicity. Alveolar hemorrhage, necrosis, and, eventually, cavity formation, are commonly seen.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPneumonia caused by Pseudomonas aeruginosa infection
frPneumonie due à une infection à Pseudomonas aeruginosa
dePneumonie durch Pseudomonas aeruginosa-Infektion
esNeumonía causada por infección por pseudomonas aeruginosa
itPolmonite dovuta a infezione da Pseudomonas aeruginosa
nlPneumonie veroorzaakt door Pseudomonas aeruginosa-infectie
ptPneumonia por Pseudomonas aeruginosa serótipo O11
plZapalenie płuc wywołane przez Pseudomonas aeruginosa
csPneumonie způsobená infekcí Pseudomonas aeruginosa
ukПневмонія, спричинена інфекцією Pseudomonas aeruginosa
zh铜绿假单胞菌感染性肺炎
trPsödomonas aeruginosa enfeksiyonunun neden olduğu pnömoni

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10J15.1NTBTattributedvalidated
ICD-11CA40.05Especificvalidated
MONDO0037398Evalidated
UMLSC0920182Evalidated
GARD13613Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalence1-5 / 10 00050 / 100 000EuropeValue and classValidatedEuropean Medicines Agency[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card