Sudden sensorineural hearing loss
Synonyms: Secondary acute sensorineural hearing loss
- Type
- Particular clinical situation in a disease or syndrome
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
A rare otorhinolaryngologic condition characterized by sudden hearing loss of at least 30 decibels across three contiguous frequencies, within 72 hours or less, due to acute damage to the cochlear hair cells, resulting from acoustic trauma or mechanical trauma during surgery, or occurring without any known cause. The hearing loss may affect one or both ears. Typical concomitant symptoms are aural fullness, tinnitus, and vertigo. Patients may fully recover or remain with hearing loss of variable intensity.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Sudden sensorineural hearing loss | Secondary acute sensorineural hearing loss |
| fr | Perte auditive neurosensorielle brutale | Perte auditive neurosensorielle aigüe brutale |
| de | Plötzliche Schallempfindungsschwerhörigkeit | Sekundärer akuter sensorineuraler Hörverlust |
| es | Hipoacusia neurosensorial súbita | Hipoacusia neurosensorial aguda secundaria |
| it | Perdita di udito neurosensoriale improvvisa | Perdita di udito neurosensoriale acuta secondaria |
| nl | Plotseling sensorineuraal gehoorverlies | Secundair acuut sensorineuraal gehoorverlies |
| pt | Perda auditiva neurossensorial de início súbito | Perda auditiva neurossensorial aguda secundária |
| pl | Ostra czuciowo-nerwowa utrata słuchuna skutek ostrego urazu akustycznego lub nagła głuchota lub operacja powodująca uraz akustyczny | Nagła głuchota czuciowo-nerwowa |
| cs | Akutní senzorineurální ztráta sluchu způsobená akutním akustickým traumatem anebo náhlou hluchotou nebo akustickým traumatem indukovaným operací | = en |
| uk | Раптова нейросенсорна приглухуватість | Вторинна гостра сенсоневральна приглухуватість |
| zh | 急性听觉损伤、突发性耳聋或手术所致听觉损伤致急性感音神经性听觉丧失 | |
| tr | Akut akustik travma veya ani sağırlık veya cerrahiye bağlı akustik travma nedeniyle akut sensörinöral işitme kaybı |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | H83.3 | NTBT | attributed | validated |
| ICD-11 | AB51.1 | NTBT | attributed | validated |
| MONDO | 0043373 | E | validated | |
| UMLS | C4275242 | E | validated | |
| GARD | 12927 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:68361Rare deafness
rare otorhinolaryngological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | 1-5 / 10 000 | 40 / 100 000 | Europe | Value and class | Validated | European Medicines Agency 2018[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/90059
- This record as JSON: /data/d/90059.json