Superior limbic keratoconjunctivitis
Synonyms: SLK · Theodore superior limbic keratoconjunctivitis · Theodore syndrome
- Type
- Disease
- Group
- Disorder
- Status
- active
A rare disorder of the anterior segment of the eye characterized by unilateral or bilateral, chronic and recurrent inflammation affecting the upper tarsal and bulbar conjunctiva, as well as the superior limbus, manifesting as a papillary reaction on the upper tarsal conjunctiva, thickening and folding of redundant superior bulbar conjunctiva, and superficial punctate epithelial keratitis with or without filament formation near the superior corneal limbus. Middle-aged women are most commonly affected and present with foreign body sensation, frequent blinking, burning sensation, and pruritus, among others.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Superior limbic keratoconjunctivitis | SLK · Theodore superior limbic keratoconjunctivitis · Theodore syndrome |
| fr | Kératoconjonctivite limbique supérieure | Kératoconjonctivite limbique supérieure de Théodore · Syndrome de Théodore |
| de | Keratokonjunktivitis, limbische superiore | SLK · Superiore limbische Keratokonjunktivitis Theodore · Theodore-Syndrom |
| es | Queratoconjuntivitis límbica superior | Queratoconjuntivitis límbica superior de Theodore · SLK · Síndrome de Theodore |
| it | Cheratocongiuntivite limbica superiore | Cheratocongiuntivite limbica superiore di Theodore · SLK · Sindrome di Theodore |
| nl | Superieure limbische keratoconjunctivitis | SLK · Superieure limbische keratoconjunctivitis van Theodore · Syndroom van Theodore |
| pt | Queratoconjuntivite límbica superior | |
| pl | Górne rąbkowe zapalenie spojówki i rogówki | Górne rąbkowe zapalenie spojówki i rogówki Theodore'a · SLK · Zespół Theodore'a |
| cs | Horní limbická keratokonjunktivitida | SLK · Theodorova horní limbická keratokonjunktivitida · Theodorův syndrom |
| uk | Верхній лімбічний кератоконюнктивіт | SLK · Верхній лімбічний кератоконюнктивіт Теодора · Синдром Теодора |
| zh | 上角膜缘角膜结膜炎 | Theodore上缘角膜结膜炎 |
| tr | Süperior limbik keratokonjunktivit | SLK · Theodore sendromu · Theodore süperior limbik keratokonjunktivit |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | H16.2 | NTBT | attributed | validated |
| ICD-11 | 9A60.Y | NTBT | index | validated |
| MONDO | 0019504 | E | validated | |
| UMLS | C0339229 | E | validated | |
| GARD | 10940 | E | validated | |
| MedDRA | 10078410 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:519280Rare conjunctivitis
rare ophthalmic disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/88633
- This record as JSON: /data/d/88633.json