Extragonadal teratoma
- Type
- Disease
- Group
- Disorder
- Status
- active
Extragonadal teratoma is an extremely rare, benign or malignant germ cell tumor characterized, clinically, by a teratoma presenting in an extragonadal location (e.g. retroperitoneum, mediastinum, craniofacial or sacrococcygeal region, intraosseous, solid organs) and, histologically, by displaying well-differentiated structures, as well as immature elements. Presenting symptoms are variable depending on size and location of tumor.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Extragonadal teratoma | |
| fr | Tératome extragonadique | |
| de | Teratom, extragonadales | |
| es | Teratoma extragonadal | |
| it | Teratoma extragonadico | |
| nl | Extragonadaal teratoom | |
| pt | Teratoma extragonadal | |
| pl | Potworniak zewnątrzgonadalny | |
| cs | Extragonadální teratom | |
| uk | Екстрагонадна тератома | |
| zh | 性腺外畸胎瘤 | |
| tr | Ekstragonadal teratom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D48.7 | NTBT | attributed | validated |
| MONDO | 0019500 | E | validated | |
| MeSH | D013724 | E | validated | |
| UMLS | C4708601 | E | validated | |
| MedDRA | 10043276 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:99913Extragonadal non-dysgerminomatous germ cell tumor
rare neoplastic diseases; rare transplant-related disorders
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/883
- This record as JSON: /data/d/883.json