Primary adult heart tumor
Synonyms: Adult cardiac tumor · Adult heart tumor
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare disorder that manifest in adults and generally present with a variety of non-specific manifestations (depending on tumor site and infiltration) such as weight loss, exhaustion, hemorrhagic pericardial effusion, heart failure, arrhythmias, and embolisms, or that can also be asymptomatic. In adults 75% of heart tumors are benign, with myxoma being the most common benign tumor (accounting for 50-70% of all primary heart tumors) and rhabdomyosarcoma comprising 75% of malignant heart tumors. Other malignant tumors of the heart include fibrosarcoma and leiomyosarcoma.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary adult heart tumor | Adult cardiac tumor · Adult heart tumor |
| fr | Tumeur cardiaque primaire de l'adulte | |
| de | Herztumor, primärer, des Erwachsenen | Primärer kardialer Tumor des Erwachsenen |
| es | Tumor cardíaco primario del adulto | |
| it | Tumore cardiaco primitivo dell'adulto | |
| nl | Primaire harttumor bij volwassenen | Cardiale tumor bij volwassenen · Harttumor bij volwassenen |
| pt | Tumor cardíaco do adulto | |
| pl | Pierwotny guz serca dorosłych | Guz serca dorosłych |
| cs | Nádor srdce v dospělém věku | Adultní kardiální nádor |
| uk | Первинна пухлина серця у дорослих | Пухлина серця у дорослих · Пухлина серця у дорослих |
| zh | 原发性成人心脏肿瘤 | 成人心脏肿瘤 |
| tr | Primer yetişkin kalp tümörü | Erişkin kalp tümörü · Erişkin kalp tümörü |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C38.0 | NTBT | attributed | validated |
| ICD-10 | D15.1 | NTBT | attributed | validated |
| ICD-11 | 2F01 | NTBT | index | validated |
| MONDO | 0019493 | E | validated | |
| UMLS | C4275152 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:168194Rare cardiac tumor
rare cardiac diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/874
- This record as JSON: /data/d/874.json