ORPHA:854

Non-malignant and non-cirrhotic portal vein thrombosis

Synonyms: Non-cirrhotic and non-tumoral portal vein thrombosis · Non-malignant non-cirrhotic PVT

Portal vein thrombosis (PVT) is associated with acute (recent) or chronic (long-standing) thrombosis of the portal system.

Names in Orphadata languages

12 of 12 languages

Lang	Name	Synonyms
en	Non-malignant and non-cirrhotic portal vein thrombosis	Non-cirrhotic and non-tumoral portal vein thrombosis · Non-malignant non-cirrhotic PVT
fr	Thrombose portale non-maligne and non-cirrhotique	Thrombose de la veine porte non cirrhotique et non tumorale · Thrombose portale non cirrhotique et non maligne
de	Pfortaderthrombose, nicht-maligne und nicht-zirrhotische	Nicht-maligne und nicht-zirrhotische PVT · Pfortaderthrombose, nicht-zirrhotische
es	Trombosis venosa portal no maligna y no cirrótica	TVP no maligna y no cirrótica · Trombosis venosa portal no cirrótica y no tumoral
it	Trombosi non maligna e non cirrotica della vena porta	Trombosi non cirrotica e non neoplastica della vena porta · PVT non maligna non cirrotica
nl	Niet-maligne en niet-cirrotische poortadertrombose	Niet-cirrotische en niet-tumorale poortadertrombose · Niet-maligne en niet-cirrotische trombose van vena portae · Niet-maligne niet-cirrotische VPT
pt	Trombose da veia porta não-maligna e não-cirrótica	TVP não-maligna e não-cirrótica · Trombose da veia porta não-cirrótica e não-tumoral
pl	Pierwotna zakrzepica żyły wrotnej	= en
cs	Trombóza portální žíly	= en
uk	Первинний тромбоз воротної вени	Нециротичний тромбоз портальної вени
zh	原发性门静脉血栓形成	非肝硬化门静脉血栓
tr	Primitif portal ven trombozu	Sirotik olmayan portal ven trombozu

Definition in:

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
ICD-10	I81	NTBT	attributed	validated
ICD-11	DB98.3	NTBT	specific	validated
MONDO	0019431	E		validated
UMLS	C0155773	E		validated
MedDRA	10036206	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

0 direct

Orphanet records no gene directly on this code.

5 records

Type	Class	Value	Area	Qualification	Validation	Source
Point prevalence	1-9 / 100 000	3.7 / 100 000	Sweden	Value and class	Validated	21039677[PMID]
Annual incidence	1-9 / 1 000 000	0.7 / 100 000	Sweden	Value and class	Validated	21039677[PMID]
Point prevalence	Unknown	—	Europe	Class only	Validated	ORPHANET
Annual incidence		2.75 / 100 000	Italy	Value and class	Validated	28180235[PMID]
Annual incidence	1-9 / 100 000	1.72 / 100 000	Europe	Value and class	Validated	21039677[PMID]_28180235[PMID]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

Orphanet has no HPO annotation for this code in this release.