raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:715318

Intracranial dural arteriovenous fistula

Synonyms: Dural AVF

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult, Childhood
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enIntracranial dural arteriovenous fistulaDural AVF
frFistule artério-veineuse durale intracrânienneFAV durale
deIntrakranielle durale arteriovenöse FistelidAVF
esFístula arteriovenosa dural intracranealFAV dural
itFistola arterovenosa durale intracranicaFAV durale · AVF durale
nlIntracraniële durale arterioveneuze fistelDurale AVF
ptAcquired intracranial dural arteriovenous fistula
plWewnątrzczaszkowa przetoka tętniczo-żylna opony twardej= en
csIntracranial dural arteriovenous fistula= en
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card