raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:698063

Fibromuscular dysplasia of the visceral arteries

Synonyms: Visceral fibromuscular dysplasia

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enFibromuscular dysplasia of the visceral arteriesVisceral fibromuscular dysplasia
frDysplasie fibromusculaire des artères viscérales
deFibromuskuläre Dysplasie der viszeralen ArterienViszerale FMD
esDisplasia fibromuscular de las arterias visceralesDisplasia fibromuscular visceral
itDisplasia fibromuscolare delle arterie visceraliDisplasia fibromuscolare viscerale
nlFibromusculaire dysplasie van viscerale arteriënViscerale fibromusculaire dysplasie
ptFibromuscular dysplasia of the visceral arteries
plFibromuscular dysplasia of the visceral arteries= en
csFibromuscular dysplasia of the visceral arteries= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10I77.3NTBTattributednot yet validated
ICD-11BD41.0NTBTattributednot yet validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card