raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:697986

Congenital peritoneal encapsulation

Synonyms: CPE · Peritoneal encapsulation syndrome

Type
Malformation syndrome
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult, Antenatal
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enCongenital peritoneal encapsulationCPE · Peritoneal encapsulation syndrome
frEncapsulation péritonéale congénitale
deKongenitale peritoneale EinkapselungCPE · Verkapselungssyndrom des Peritoneums
esEncapsulación peritoneal congénitaEPC · Síndrome de encapsulación peritoneal
itIncapsulamento peritoneale congenitoCPE · Sindrome da incapsulamento peritoneale
nlCongenitale peritoneale inkapselingCPE · Peritoneaal inkapselingssyndroom
ptCongenital peritoneal encapsulation
plCongenital peritoneal encapsulation= en
csCongenital peritoneal encapsulation= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10K66.8NTBTattributedvalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Cases/families50 casesWorldwideCase(s)Validated31148901[PMID]
Point prevalence<1 / 1 000 000—WorldwideClass onlyValidated31148901[PMID]_ORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card