raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:697132

Lymphoepithelial cyst of the pancreas

Synonyms: Pancreatic lymphoepithelial cyst

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enLymphoepithelial cyst of the pancreasPancreatic lymphoepithelial cyst
frKyste lymphoépithélial du pancréasKyste lymphoépithélial pancréatique
deLymphoepitheliale Zyste der BauchspeicheldrüsePankreatische lymphoepitheliale Zyste
esQuiste linfoepitelial de páncreasQuiste linfoepitelial pancreático
itCisti linfoepiteliale del pancreasCisti linfoepiteliale pancreatica
nlLymfo-epitheliale cyste van pancreas
ptLymphoepithelial cyst of the pancreas
plLymphoepithelial cyst of the pancreas= en
csLymphoepithelial cyst of the pancreas= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10K86.2NTBTattributedvalidated
ICD-11DC30.0NTBTattributedvalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Cases/families200 casesWorldwideCase(s)ValidatedORPHANET
Point prevalence<1 / 1 000 000—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card