raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:662721

Placenta accreta spectrum disorder

Synonyms: AIP · Abnormally invasive placenta · PAI · PAS · Placenta accreta spectrum

Type
Disease
Group
Disorder
Inheritance
Not applicable
Status
active

A rare disorder related with pregnancy characterized by an abnormally invasive placenta that fails to detach spontanously from the uterine wall during delivery. Placenta that partially or totally attached to uterine wall, risk to cause massive and life-threatening bleeding if forced to remove. Prenatal diagnosis is essential, however difficult, to reduce maternal and fetal morbidity. Major risk factors are uterine surgery and uterine scar secondary to cesarean delivery.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enPlacenta accreta spectrum disorderAIP · Abnormally invasive placenta · PAI · PAS · Placenta accreta spectrum
frTroubles du spectre du placenta accretaPAS · Placenta anormalement invasif · Spectre du placenta accreta
dePlacenta accreta-Spektrum-StörungAIP · Abnorm invasive Plazenta · PAI · PAS · Placenta-accreta-Spektrum
esTrastorno del espectro de placenta acretaEspectro de placenta acreta · Placenta anormalmente invasiva
itMalattia dello spettro della placenta accretaAIP · PAI · PAS · Placenta abnormemente invasiva · Spettro della placenta accreta
nlPlacenta accreta spectrumstoornisAIP · Abnormaal invasieve placenta · PAI · PAS · Placenta accreta spectrum
ptEspectro clínico de placenta acretaPlacenta anormalmente invasiva · AIP · Espectro clínico de placenta acreta · PAI · PAS
plSpektrum zaburzeń z łożyskiem przyrośniętym= en
csPorucha placenta accreta spectrum= en
ukПорушення спектру прикріплення плацентиАномально інвазивна плацента · AIP · PAI · PAS · Спектр прикріплення плаценти

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10O43.2NTBTattributedvalidated
ICD-11JA8A.2NTBTattributedvalidated
MONDO0005916Evalidated
MONDO5916Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card