raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:658602

Transplant-related bronchiolitis obliterans

Synonyms: BOS · Bronchiolitis obliterans syndrome

Type
Disease
Group
Disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enTransplant-related bronchiolitis obliteransBOS · Bronchiolitis obliterans syndrome
frBronchiolite oblitérante post-greffeSyndrome de bronchiolite oblitérante
deBronchiolitis obliterans, transplantationsbedingteBOS · Bronchiolitis obliterans-Syndrom
esBronquiolitis obliterante secundaria a trasplanteSBO · Síndrome de bronquiolitis obliterante
itBronchiolite obliterante correlata al trapiantoSBO · Sindrome della bronchiolite obliterante
nlBronchiolitis obliterans gerelateerd aan transplantatieBOS · Bronchiolitis obliterans-syndroom
ptBronquiolite obliterante transplante-relacionadaBOS · Síndrome de bronquiolite obliterante
plZarostowe zapalenie oskrzelików związane z przeszczepem= en
csBronchiolitis obliterans související s transplantací= en
ukОблітеруючий бронхіоліт, повязаний з трансплантацієюBOS · Синдром облітеруючого бронхіоліту
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10Y83.0NTBTattributedvalidated
ICD-11CA26.0NTBTattributedvalidated
MONDO0958127Evalidated
MONDO958127Evalidated
UMLSC5574736Evalidated
MedDRA10083303Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card