raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:645626

Adermatopathic dermatomyositis

Synonyms: Dermatomyositis sine dermatitis

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enAdermatopathic dermatomyositisDermatomyositis sine dermatitis
frDermatomyosite sine dermatitis
deDermatomyositis, adermatopathischeDermatomyositis ohne Dermatitis
esDermatomiositis adermatopáticaDermatomiositis sin dermatitis
itDermatomiosite adermopaticaDermatomiosite senza dermatite
nlAdermatopathische dermatomyositis= en
ptDermatomiosite adermatopáticaDermatomiosite sine dermatite
plAdermatopatyczne zapalenie skórno-mięśniowe= en
csAdermatopatická dermatomyozitida= en
ukАдерматопатичний дерматоміозитДерматоміозит синегнійний дерматит
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10M33.1NTBTattributedvalidated
ICD-114A41.0NTBTattributedvalidated
MONDO0957458Evalidated
UMLSC5816708Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

  • ORPHA:221Dermatomyositis
    rare neurological diseases; rare skin diseases; rare renal diseases; rare systemic and rheumatological diseases; rare transplant-related disorders

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card