raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:645617

Amyopathic dermatomyositis

Synonyms: Dermatomyositis sine myositis

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enAmyopathic dermatomyositisDermatomyositis sine myositis
frDermatomyosite amyopathiqueDermatomyosite sine myositis
deDermatomyositis, amyopathischeDermatomyositis ohne Myositis
esDermatomiositis amiopáticaDermatomiositis sin miositis
itDermatomiosite amiopaticaDermatomiosite senza miosite
nlAmyopathische dermatomyositis= en
ptDermatomiosite amiopáticaDermatomiosite sine miosite
plAmiopatyczne zapalenie skórno-mięśniowe= en
csAmyopatická dermatomyozitida= en
ukАміопатичний дерматоміозитДерматоміозит синус-міозит
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO0043317Evalidated
MeSHC538250Evalidated
UMLSC0406645Evalidated
GARD9907Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

  • ORPHA:221Dermatomyositis
    rare neurological diseases; rare skin diseases; rare renal diseases; rare systemic and rheumatological diseases; rare transplant-related disorders

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card