ORPHA:642071

Primary pulmonary vein stenosis

Synonyms: Congenital pulmonary vein stenosis · PPVS

Orphadata ships no English definition for this code.

Names in Orphadata languages

10 of 12 languages

Lang	Name	Synonyms
en	Primary pulmonary vein stenosis	Congenital pulmonary vein stenosis · PPVS
fr	Sténose primaire des veines pulmonaires	Sténose congénitale des veines pulmonaires
de	Pulmonalvenenstenose, primäre	PPVS
es	Estenosis de vena pulmonar primaria	PPVS
it	Stenosi primaria delle vene polmonari	PPVS
nl	Primaire stenose van vena pulmonalis	PPVS · Primaire stenose van longader
pt	Estenose primária da veia pulmonar	PPVS
pl	Pierwotne zwężenie żył płucnych	= en
cs	Primární stenóza plicní žíly	= en
uk	Первинний стеноз легеневої вени	Вроджений стеноз легеневої вени · PPVS

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
ICD-10	Q26.8	NTBT	attributed	validated
ICD-11	LA86.3	E	specific	validated
MONDO	0957433	E		validated
UMLS	C0265915	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

ORPHA:3188Congenital pulmonary veins atresia or stenosis
rare developmental anomalies during embryogenesis; rare cardiac malformations; rare respiratory diseases; rare circulatory system diseases; rare transplant-related disorders

No children.

0 direct

Orphanet records no gene directly on this code.

0 records

No prevalence record in this release.

Orphanet has no HPO annotation for this code in this release.