raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:63443

Rare epithelial tumor of stomach

Synonyms: Rare gastric epithelial tumor

Type
Category
Group
Group of disorders
Inheritance
Multigenic/multifactorial, Not applicable
Age of onset
Adult
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enRare epithelial tumor of stomachRare gastric epithelial tumor
frTumeur épithéliale rare de l'estomacTumeur épithéliale gastrique rare
deSeltener epithelialer Tumor des Magens
esTumor epitelial raro de estómagoTumor epitelial gástrico raro
itTumore epiteliale raro dello stomacoTumore epiteliale gastrico raro
nlZeldzame epitheliale tumor van maagZeldzame epitheliale maagtumor
ptCancro gástricoCancro do estômago
plRzadki nabłonkowy guz żołądka= en
csVzácný epiteliální tumor žaludkuVzácný žaludeční epiteliální tumor
ukРідкісна епітеліальна пухлина шлункаРідкісна епітеліальна пухлина шлунка
zh罕见胃上皮性肿瘤罕见胃上皮瘤
trNadir mide epitel tümörüNadir mide epitel tümörü
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO18972Evalidated
UMLSC5680118Evalidated
MedDRA10017758Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (3):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

7 records
TypeClassValueAreaQualificationValidationSource
Annual incidence1-5 / 10 00018.6 / 100 000EuropeValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Lifetime Prevalence1-5 / 10 00049.17 / 100 000EuropeValue and classValidated22033323[PMID]_RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0007.5 / 100 000United StatesValue and classValidatedNational Cancer OTHERitute 2010[OTHER]
Point prevalence1-5 / 10 00024 / 100 000United StatesValue and classValidatedNational Cancer OTHERitute 2010[OTHER]
Annual incidence1-5 / 10 00011.2 / 100 000United KingdomValue and classValidatedNational Cancer Intelligence Network 2006[OTHER]
Point prevalence1-9 / 100 0003.9 / 100 000United KingdomValue and classValidatedNational Cancer Intelligence Network 2006[OTHER]
Point prevalence1-9 / 100 000—EuropeClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card